Eisenmenger syndrome: Okú, tohu, Diagnosis, Treatment

I roto i te mafatu i roto i te whānui me te i roto i malformations congenital i ngā i te kau i reira e kua tekau o "iti" tikanga. E whakaahuatia ētahi o ratou mo te wa roa, me te pai tukinotia i wā ante- me fā'ele'i, engari te nuinga kei te rapu tonu mo te kairangahau. Ko tētahi o ratou ko mate Eisenmenger. tāutuhia te syndrome i roto i te tīmatanga o te rau tau rua tekau i te tākuta tamariki Austria tairanga, me te faaite i teie nei tona ingoa.

whakamāramatanga

syndrome Eisenmenger (Eisenmenger) - tenei ofatiraa whanaketanga mua o te uaua ngakau, e ngā te aroaro o te koha i roto i te pakitara wehewehe i waenganui i nga ventricles, te haoraora tūnga otzerkalennoe, me te whakanui ake i te rahi o te mānawanawa tika. Aua'e, e taea te pai whakahaeretia tenei koha, a anō tupu tamariki, me te whakawhanake i roto i te ara ano rite ratou hoa.

tatauranga

I te kau, e pā ana ki e rima ōrau o te wā katoa o kōhikohiko cardiac i roto i ngā tamariki e Eisenmenger syndrome. mate ngakau congenital taea te wehea ki ētahi atu mate ngakau o hou, me ngā tamariki taitamariki. Kua ngā ētahi tākuta kāore tetahi raruraru hemodynamic i roto i tenei syndrome.

Syndrome matatini ranei

Tohatoha matatini motuhake, me te Eisenmenger syndrome. Syndrome - he ti'araa maumaui uncorrected o te tohanga o te toto ki te hipa i te whanaketanga i waenganui i nga kōwhao o nga ventricles ngakau. He matatini ngā disorders motuhake kitea i roto i te kukune fanau ranei.

etiology

Ko te tukanga o te āhua o hanga e tenei syndrome te, tae noa ki te mea e mohiotia te mutunga, kei te tamata tonu aivanaa me tākuta ki te kitea he whakamārama. Heoi, whakahaere rawa pai ratou ki te titiro i te āhuatanga e tika ana ki e puta Eisenmenger matatini. Ka taea te wehea nga take ki e rua ngā kāwai: pānga ā-, ranei ira, a waho ranei taiao.

1. Kōrero e pā ana ki te tuku tuku tika o tenei mate e kore e taea e, engari ki te he te whanaunga matamua aho-rua ranei raruraru hakari o te hanganga o whekau faufaa, i reira te mea tonu he tupono e te tamaiti whakatika ratou.
2. Pau i roto i te wā whānautanga. Ko te kāwai mōrearea ngā wahine hapu e noho ana i roto i nga pa nui, mahi i roto i te mahi mōrearea e pā ana ki täoke matū tinana ranei ranei.
3. Tango rongoa. Ētahi taero mōrearea ki te tango i roto i te whanautanga tamariki. Na reira, i mua i haputanga ranei i roto i te wiki tuatahi i muri i kia runanga te obstetrician ki nga moni riro katoa. Ahakoa, ki te te reira noa te papa ānini.
4. Ko te whakamahi o huaora me tāpiringa kai o te kounga nanakia. Ko te tikanga e kinokore enei matū, engari i roto i ngā take onge taea meinga ratou e kore kua kino ki te fariiraa ano i hanga i te kōhiwi o te tamaiti o tona whekau ranei.
5. Ko te aroaro o tetahi o nga matua-ki-wā roa-mate ma'i.

O te akoranga, e kore e enei take tohu āta i runga i Eisenmenger syndrome. Tohu, e kōrero tona tātaritanga me te maimoatanga i raro.

pathogenesis

A, no te he tangata e hakari taua āhuatanga kikokiko, kia tino reira ka kia raruraru i roto i te tohanga toto. Nā ki te aroaro o tino koha ventricular septal, me te hoki o te tūranga he o te haoraora he venous whakauru me te toto te pūtahi o roto i te kōhao ngakau. Ie i hanga whakanekeneke me whakanekeneke i mahue ki matau. Neke atu i te wa, te pēhanga i roto i te piki kātua pūkahukahu, i ētahi wā kia ara nui te reira i te hunga i roto i te haoraora. Tenei, i roto i te tahuri, arata'i ki te spasm pūpū o oko toto iti i roto i te tohanga pūkahukahu. Te whakawhanake i takawhita pūkahukahu. Ki te pumau reira he wa roa, ka i reira he he thickening e vai o nga taiepa o tōiti me stasis toto puta i roto i te pūkahukahu.

ngā kaihaumanu "ma" a "puru" Eisenmenger syndrome. I roto i te take tuatahi, ko te whakanekeneke i roto i tona putanga matarohia, e ko, i mahue ki matau, a i roto i te tuarua - i runga i te anga ke.

tohu

I roto i nga kohungahunga, me tamariki taitamariki tohu pānui motuhake he uaua. whanaketanga tinana, me te hinengaro o te tamariki e kore e tukua e. Ki te puta tau whakanuku ritenga, ka te tangata hāhā o te manawa, puru tapatoru nasolabial me pito, te rohirohi, palpitations ranei arrhythmia mamae nga korero o te momo angina. Angamaheni Ko te āhuatanga e tango tūroro ki te whakaiti i te tohu - squatting. Na riro te reira māmā ki te manawa.

O te mau ma'i noa maha taea rongo amuamu o pāhoahoa, nosebleeds, me te maremare ake toto. Ka taea e koe te huri i te reo e tika ana ki te kōpeketanga o nga hopearaa karere o te pera dilated. E mea pinepine e taea tetahi mau pathologies rite protrusion o te momo pouaka o koropuku, me te huri i nga phalanges kāpeka o te maihao rite ngā waewae, tuhu ki te kore manawa, i huaina nei ko syndrome o Eisenmenger. Take, tohu, tātaritanga mohiotia reira ki nga mafatu.

kia uaua te matatini i Bronchitis, kakā, endocarditis kitakita etiology, toto i nga pūkahukahu, a tae noa whawhai ratou ngakau. Te kore maimoatanga, e kore te mea neke atu i te toru tekau nga tau te tümanako i roto i te tūroro tangata ora.

tātaringa

Kia aroha mai, ka whakakitea te whakamātautau noa te mate e kore e taea. I roto i te tikanga ki te whakaū i te tātaritanga pōhēhē, e rapu tikanga motuhake o te rangahau:

1. X-hihi o te pouaka, e ka whakaatu i te huringa ataata o takiwa ngakau me oko nui.
2. i naia Angiography rite atahanga technique o te whanaketanga iaia whakamahia te maha, engari i roto i tenei take e kore ko reira motuhake, a taea anake kitea huringa mātanga rawa mātanga.
3. ECG te heheu i roto i taua take, ki te te puritia reira i raro i te Holter aroturuki. Katahi te mōhiohio te tākuta e kore e waiho e rima meneti Tuhinga, a mo te ki tonu ra, a ka taea ki te tāutu i ngā rerekētanga i roto i te auau huamoni ia.
4. Echocardiography - ultrasound o te ngakau, ko te. He tikanga pai hoki te kimi hē i roto i te kōwhao o te ngakau, me te toto disorders.
5. catheterization cardiac, i roto i tenei take - te tikanga tino manakohia, me te pono o te rangahau. E tauturu te reira ki te tāutu i ngā hē katoa, whakatau i te āhuatanga o te ngakau kotahi, me te whakawhanake i te maimoatanga.

Ko te he uaua taua ki te tātari Eisenmenger syndrome. Tohu (mate multistage maimoatanga me te wā-kai) ke ana tona māuiuitanga nonspecific te rite te mate noa, me te mawhiti te aro o kaimahi whānui.

maimoatanga

Ahakoa te aroraa tonu i waenganui i tākuta me rata, i roto i te take o tenei mate, whakaae ratou e hiahia tautooraa tahi ki te kia tukinotia rite maimoatanga momo i roto i te kore e hoatu ano te pānga e hiahiatia ana, a kore e taea wawe whakarato murunga pūmau. Na reira, kua hangaia he huinga o mehua ki te whakakore i te syndrome Eisenmenger:

1. Tahe (ki te takawiri hou, i huaina tenei ko te "phlebotomy"). tikanga Simple me te raruraru-free. Kei te whakamahia te reira i roto i te tūroro ki te māuiuitanga tamatahia o nga wa, he tokorua he tau. I mua a muri te tukanga tika whakaritea e te pokey o toto , me te pūtoto taumata.
2. Whakamahi o te hāora hau. Whakamahia hei therapy tānga ki te mahi ki cyanosis me hypoxia tuarua. I tua atu, to ratou he pānga psychosomatic i runga i nga tūroro.
3. Anticoagulants. e kore e ratou i te taumata rawaka o te taunakitanga rite taea ki te tiki i roto o te paraipanatia ki te ahi, a hei utu o thinners toto ki te tiki i tona nesvorachivaemost tonu.
4. Ētahi atu rongoā:
   - Diuretics mō te tango i edema pūkahukahu;
   - ki te rongoā te whakapai ake hemodynamics.
5. Technique hāparapara:
   - pacemaker ki te utu mo te arrhythmia;
   - oti tango o te katinga septal koha ventricular me te whakanekeneke rerekē.

Tofu pehea ki te hamani Eisenmenger syndrome kia whakatutuki ki tō tākuta ara e rave rahi tohunga ranei. Na me pehea ki te hoatu i te taurangi o te angitu e kore e taea e tetahi tikanga kotahi.