Hauora, Diseases me ngā Here
Lymphomas T pūtau-: ngā momo, tohu, te tātaritanga, maimoatanga me te waitohunga
lymphomas T pūtau-tino maha pāngia i roto i tūroro i roto i te tau tawhito, engari e hoki taiohi me tamariki e pängia ana ki te mate. Na mamae tangata i reira atu maha atu i te wahine.
He aha te mea he lymphomas T-pūtau
Lymphoma - he lesion mārere kiko lymphoid me ētahi atu whēkau. I roto i te take o te lymphoma T-pūtau, ka pā te mate te kōpuku kiri me te waitinana (arā, he pūāhua epidermotropny). Ko te āhuatanga taketake e kua whai wāhi i roto i te takanga o neoplasms he T-lymphocytes (pūtau e te tikanga whakarato whakautu ārai tika). lymphoma T pūtau-(pikitia māngai i raro nei) e taea te hanga e rite ki te hua o te haaputuputuraa o te kiko pathological huānga pūtau.
Take me take takoha
- whakapapa
- Immunodeficiencies.
- Roa te rongo ki ngā āhuatanga kino: UV radiation, āpiha tukituki matū.
- āhuatanga Age (tūroro paari).
- Ko te aroaro o huaketo i roto i te rauropi (HIV, Epstein-Barr, kakā C, B, T-lymphocyte huaketo), mate intestinal.
- Ko te aroaro o irakētanga i roto i te pūnaha ārai mate, okana me te kiko transplantation, whakarite therapy immunosuppressive.
kia kia te urutanga mai (aua, whakapataritari te whanaketanga o te mate), te ahotea, pohokore, overloads io, kore ki te ū ki te tikanga o te okiokinga me te mahi i enei āhuatanga katoa.
whakarōpū
- T pūtau-kiri lymphoma. lymphomas rite te tikanga whakawhanake rite ki te hua o ngā irakētanga o lymphocytes T, ārahi ki te whakarea whakakeke o te muri, me te, no reira, pā ratou i roto i te apa o te kiriwaho. Āhuatanga e te puka kaha o te polymorph ponana lymphomas takanga (tohu, pukupuku, stains, opupu). Na amuamu nga tūroro tuatahi o te takanga o te kawe oranga ranei wahi, pae hopea e whakaahua ana ki whakatū papa, a muri i roto i te aronga puku.
- Piringa lymphoma T pūtau-. Tenei ariā ngā nga lymphomas katoa e he T-pūtau takenga NK-pūtau (anake neoplasm o teeki T-pūtau me kanisā T-lymphoblastic) ranei. Tino maha, enei lymphomas puta ki pāpaka toto, kiri, wheua wheua me whekau, me i roto i te taikiri, haaparare i kitea huringa infiltrative.
- Angioimmunoblastic lymphoma T pūtau-. whakakitea te reira rite taatiraa kiko lymphoid (i roto i te whakamātautau histological o taikiri) immunoblast me wē ngā pūtau, ki muri huringa oti o tona hanganga, me te hanganga o oko toto rerekē.
- T-pūtau lymphoma lymphoblastic. Novobrazovanie, e hāngai ana nei i runga i abnormalities o ngā pūtau T. e kore e T pūtau pakari, riro kōhikohiko i roto i te āhua o ratou karihi, ratou hohoro a uncontrollably hinga. Tūtaki tenei ahua o te lymphoma he onge. Ki te wheako koe he tātaritanga pārōnaki tauira rite ki kanisā whakapeka.
- lymphoma T pūtau-Non-Hodgkin o. tohu te reira i te rōpū nui o te pukupuku e kua tito o pakeke T-lymphocytes me e kore e hāngai ki te mate o Hodgkin (i.e., mate o Hodgkin). No ki tenei rōpū e whakaritea e whakamātautau histological (ki chlamydia i takanga kitea huānga pūtau motuhake Berezovsky-Sternberg i lymphomas kore-Hodgkin o he kahore).
atamira whanaketanga
- Ko te mate o tetahi kōpuku waitinana.
- Ko te horapa o te puku ki taikiri rua e kua kei i tetahi taha o te HWM.
- hanganga waitinana maha i runga i ngā taha e rua o te HWM.
- taikiri me whekau, aroaro o metastases i nga whatukuhu, wheua wheua, ate ranei whēkau o te wahi gastrointestinal.
tohu General
Te aroaro ngaro ranei o etahi faaiteraa haumanu tei runga i te momo o te puku, me ona wāhi. Heoi, i reira he tohu e te hunga tūturu i roto i te lymphoma T-pūtau tata katoa:
- Sweating i te po.
- Ko groundless tere mate taimaha.
- fungoides Mycosis.
- mahi iti-kōeke i roto i te pāmahana te tinana.
- ngenge auau me te tau'a.
fungoides mycosis
fungoides Mycosis - tetahi o nga mau faaiteraa tino auau e tohu lymphoma T-pūtau. Kei te kitea te reira i roto i e whitu tekau ōrau o tūroro ki tenei mate, me kua toru puka: puāwaitanga, te kāwanatanga me te erythrodermic.
fungoides mycosis Classical e tika ana i toru ngā wāhanga o te whanaketanga:
- Erythematous - i tohu haumanu rite ki te psoriasis, katoatia, me te pera i runga i. pūrongo tūroro te aroaro o stains āhua porotītaha porohita ranei, ki koi tapa, o rerekē te rahi o, ki te tae māwhero-puru, me te mata patito. Kei te maha Kei taua āhuatanga i runga i te mata, me te utumu, āta piki haere i roto i te rahinga, me te haere tahi atu wahi. e kore e taua pāpaka whakautu ki te maimoatanga me te kore e taea te pupuri hoki i te wa roa, ranei ngaro ohorere. Ano, Ka taea te ngā stains ki minamina, e kore e nei i mutu e te tikanga tikanga.
- infiltrative pātītī - puta i muri i te tau torutoru o tīmatanga. I roto i te wahi o nga stains whakatū papa i runga ki te pūrerehu, porotaka ranei nepravilnymi engari mārama rohe, papura ki tihorenga i runga i te mata. I te pae o te whakatū papa ngaro he wāhi o parauri ranei atrophy kiri. piki minamina, riro te reira fuu. He he he mate taimaha tere, me te kirika, kia lymphadenopathy reira.
- Puku - i runga i-pae ranei whakatū papa i runga i te kiri e kore e reira puta ke te ahua o mātotoru puka puku porohita ongonoa whero me te kowhai ranei paku papatahi āhua, Ahakoa he pōtae mushroom. Ko te diameter o taua ngā pae maunga i tetahi ki te e rua tekau mitamano, a kia kia rerekē te tau. A, no te huna i te puku te, mariao fakamamahi i hanga i roto i tona wahi, i te hōhonu o e taea tae te fascia wheua ranei. Nuinga o ngā wā pā te kōateate, taikiri, pūkahukahu me te ate. haurangi Narostaet me te ngoikore. mate Tūroro o kore ngakau, amyloidosis, kakā.
āhuatanga puka Eritrodermicheskoy e te putanga o te narostaet fakamamahi minamina, whero me te puku, te ahua o te confluent wahi erythematous-squamous, hyperkeratosis o nga kapu me nikau, me te huruhuru mate. Kia rahi atu taikiri katoa i roto i te axillary, inguinal, femoral me ngā wāhi cubital. A, no te e kitea e ratou plotnoelastichnye pākete waitinana palpation ongonoa e kore soldered ki te kopa e karapoti (kiri). kite Lihodradka (ki runga, ki te 39 nga nekehanga), mate taimaha, sweats po, me te rohirohi. Ko taea putanga whakamate, ka hono exacerbating haurangi me te kore ngakau.
I roto i te aroaro o te puka te kāwanatanga i runga i te kiri hauora i reira he whakatū papa maha, pae hopea whiwhi harater mārere. puta te mate i roto i te tūroro i roto i te tau.
faaiteraa haumanu o lymphomas waihakihaki
maha puta lymphoma T pūtau-o te kiri ki te puipuitua o te maimoatanga roa-ngā, me te tano ore o te mate Dermatological. Whakapataritari tona tupu e taea herpes huaketo, radiation, tīkākā, me te pera i runga i. lymphomas rite puta i roto i rua ngā wāhanga: tuatahi (paetata tukanga e i roto i te kiri), Tuarua (ina ko te hua o te lymphocyte kookuhutanga o nga whekau pāpaka kiri).
Ko te tohu matua ko:
- ponana kiri Polymorphic.
- Rising minamina.
- Ko te aroaro o te iti, āhuatanga flat i roto i te puka nodular.
- Āhua whakatū papa kowhai, muri whakaahua ki whitiki o hyperpigmentation me atrophy (ka puka tohu).
- Ko te pikitia haumanu Ahakoa psoriasis (i te momo melkouzelkovoy).
- Maroke, puku, whero me te etahi tihorenga o te kiri (ki momo erythrodermic o mate).
Tohutanga o lymphomas piringa
Tei mate hauora i runga i te atamira me te momo o te tukanga pathological.
Āhuatanga e te hua o te kiko lymphoid i te kaki, tapatapa, me te axillary rohe.
Tūroro amuamu o sweating nui, nui mate taimaha, kore o te hiahia, ngoikore whānui, kirika, a i roto i te aroaro o te kōateate rahi me te ate (i te mea tino noa) - i te hāhā o te manawa, mare recurrent me te mana'o o te pouri i roto i te kopu.
tātaringa
- Tuhinga, kohinga o amuamu me anamnesis matepukupuku rānei.
- toto General me te tātari mimi.
- mataora toto, me te whakamātautau hoki paturopi ki te wheori kakā.
- He unuhanga o te tīpona waitinana pakaru (e taea ki a koe te manatoko i te tātaritanga o te lymphoma T-pūtau).
- US.
- Mua.
- CT.
- tinana Onkoskrining.
- ako Immunofenotipirovannoe.
- tätari ira rāpoi.
- tātari Cytogenetic.
therapy
Maimoatanga o te lymphoma T-pūtau tei runga i te puka, me te wāhanga o te tukanga.
Hei tauira, mo nga fungoides atamira mycosis erythematous kore e whakaritea anticancer motuhake therapy, me nga corticosteroids waho, me te interferon whakamahia te.
Ko te maimoatanga anti-puku, ko te ki te kawe i roto i te hahau, me te iraruke.
I roto i te runga ki te ahua o te mate (mangere, pukuriri, me tino pukuriri) whakaritea e te roa, me te hanganga o te maimoatanga, me te whakanohonoho.
e kore te lymphoma mangere tukinotia, engari anake auau kitea ki te kauneke i te tukanga, te huri i te tātai.
I roto i te maimoatanga o pukuriri momo o te whakamahi huinga o taero chemotherapeutic me Rituximab (antibody monoclonal).
A, no te haere mai te reira ki lymphomas tino pukuriri, whakahau taero e kua whakamahia i roto i te maimoatanga o leukemias whakapeka.
Tino maha, ngā hahau ki transplantation kakau pūtau.
Heoi, ko te maimoatanga whai hua tino hoki lymphoma ko ki te whakahaere i te therapy toru tekau radiation (rite whakaahuatia i roto i te Elekta Synergy), a i muri i te fariiraa i te āpiha chemotherapeutic.
Pōauautanga te fariiraa i āpiha chemotherapeutic kia ngā: pūkahukahu, uma, a na reira i runga i. kia uaua radiation therapy i te whanaketanga o te atherosclerosis coronary.
I muri i te maimoatanga angitu ko te whakanohonoho herea.
lymphoma T pūtau-: matapae
- A, no te kitenga wā o te mate (wāhanga tuatahi) me te taumahi o te maimoatanga-tau e rima auau ora rawaka he waru tekau-rima ōrau, me hoki tūroro pediatric - ki iwa tekau ōrau.
- No nia i lymphoma angioimmunoblastic whakaaroa matekiri. Ko te tümanako ora toharite i roto i te tūroro ki te tātaritanga taua he e rua anake me te hawhe - e toru nga tau. Ko te tere oranga o anake kotahi-toru o te tūroro i te wā o e rima nga tau.
- I roto i te aroaro o te puka waitohunga T-lymphoblastic tei runga i te aroaro / ngaro o te lesion o te hinu wheua wheua. Ki te te kore pāngia te hinu wheua wheua, he te tikanga pai te putanga. Kore, ka taea e te tika ana te whakapai ake i roto i te ōrau e rua tekau anake o tūroro.
- Tei waitohunga me te ora mushroom avium i runga i te puka, me te wāhanga o te tukanga. Ko te kupu, ka te pae oranga puka - ki runga ki te tekau tau, me te waitohunga kino i roto i te take o te rironga o te kakā, a pera i runga i; puka eritrodermicheskoy sorovozhdaetsya hono ngā pōauautanga hua i roto i te mate puta i roto i rua - e rima nga tau; i te puka poutoa o te waitohunga rawakore, puta mate i roto i te tau.
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