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Tohu e pā ana ki hemolytic-uremic syndrome, me tona maimoatanga

Na, he aha e hiahia ana koe ki te mohio te tuatahi o te katoa e tika ana ki te syndrome hemolytic-uremic (haapotohia - Hus). Doctors huanga tenei mate te nuinga ki te tohu e toru: whakapeka täkihi, anemia hemolytic, thrombocytopenia. Me kï reira e te nuinga o te āhuatanga muri whakakitea tino mārama. pāngia te mate te matua i roto i ngā tamariki taitamariki.

take ka taea

Ko te āhuatanga matua e pā ana ki hemolytic-uremic syndrome - he tauhohenga pāwera ki rongoā, me te te mate viral. Ko reira arorau e tīmata te mate ki te whakawhanake i muri i whakapeka romahā me te puku mate ranei i roto i te tūroro te whiwhi paturopi. Ki te whakaaro ki te pathogenesis o Hus, te faatura tenei i roto i, kua piri te faufaa rahi ki te aroaro o tauhohe autoimmune. I roto i ētahi wā, kia ara hoatu ratou ara ki microangiopathy pūnahanaha.

tohutanga

He aha nga tohu e te nuinga o meinga e syndrome uremic hemolytic? Me kï reira e wehea conventionally te akoranga o te mate e tākuta ki wā e toru. Tuatahi, prodromal, taea muri i te ra kotahi ki te rua wiki. Tuarua, ko te pera-ka karanga "wā raruraru" - i tetahi ki te e toru wiki. Na ka tae mai te wā whakaora (ranei te mate) o te manawanui.

Ko te wāhanga tuatahi o te mate rite te katoa rite poisoning me te haere tahi i ngā tohu pēnei i te ruaki, te mamae puku nui, korere ki tohu o te toto. Ētahi tūroro i roto i tenei wā tohua haehae, te momoe me te ara mate o te mahara. I muri i te wā prodromal i roto i tūroro maha reira mai te ora e kitea. Ki te haemolytic uraemic syndrome mātanga e pā ana rite anemia haemolytic, thrombocytopenia, me pāpaka tākihi. mea Doctors e te pikitia haumanu, rite ki te tikanga, kitea e te polymorphism. I roto i te tahi mau tūroro, kia pule tohu hemolytic raruraru, etahi - tohu o whakapeka täkihi. Common ki te wā katoa whakaaro he tohu o te anemia hemolytic - puta te reira i roto i te waenganui o te Hus.

syndrome Hemolytic-uremic i roto i ngā tamariki i roto i te wā tuarua āhuatanga e te ataahua o te kiri. I roto i te aroaro o te jaundice taea te kitea hyperbilirubinemia. whakamātautau Direct Coombs 'ko te tikanga kino, tuku iho pūtoto, te maha o erythrocytes heke. Ano, tūroro maha te toto ihu.

tātaringa

Doctors te tikanga tātari Hus, e hāngai ana i runga i toru paearu matua: te aroaro o te anemia hemolytic, thrombocytopenia te purapura me te uremia. I roto i te whānui, ko te pikitia haumanu haamana'oraa o Moshkovitsa syndrome (mate tākihi, toto clots nga oko, me pera i runga i. D.), Ki te te anake te rerekētanga e te nuinga o te whakamutunga kitea i roto i ngā tamariki pakeke, me puta mikrotrombozov te nuinga i roto i te ngakau, me te ate.

syndrome uremic Hemolytic: maimoatanga

Whakaīngoatia autoaggression - e te te whāinga matua o te maimoatanga. Ka rite ki te tikanga, ka tonoa kaiwhakaako nga ope katoa i roto i ki te ārai i coagulation intravascular. Well te āwhina heparin me prednisolone. Ki te kore e tauturu i te rongoā, kua whakaaturia reira tātari toto.

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