He aha te mea Morgagni-Stewart-Morel syndrome?

Syndrome o Morgagni-Stewart-Morel, whakaaturanga whakaahua e taea te kite i roto i tenei tuhinga, he onge - whiwhi kotahi miriona tangata mate katoa kotahi anake rau me te wha tekau. Ano, i roto i te mahi, kanohi te nuinga ngaio ki te "whatiwhatinga" o te mate, no te mea whakawhanake hia te mate mo nga tau maha, me tohu i kīia e rerekē. Tūroro i ki kia tirohia kore tetahi tākuta i mua whakakitea tino te syndrome, me te whakatau i te tātaritanga tangohia.

Ko te āhua tino o te mate tae, ka hanga reira he huringa tina heke pathological i roto i te tinana. I muri i taua, ki te āwhina i te manawanui ko ngā taea.

kōrero

Kua ata kua whakaahuatia syndrome o Morgagni-Stewart-Morel i 1762, i te wahanga o te kairangahau mate Itari Morgagni tinana e wha tekau nga wahine, ka kitea thickening o te roto o te pereti wheua frontal. I te wa ano, tuhia e ia te mōmonatanga me te huruhuru te tinana nui. kitea Morgagni tohu o te kōtuitui a fakamatala'i i taipitopito ana kitenga. I muri mai, i runga i te huinga o ngā tohu ite i taea ki te tāpiri ki te pikitia haumanu o ngā faaiteraa neurological me hinengaro Morel ko Stewart.

He aha te raruraru

Morgagni-Stewart-Morel syndrome - he mate i roto i nei te frontal kitea hyperostosis pereti wheua i roto, te mōmona me te maha o te tahi atu endocrine me pūkoro disorders. Mate i roto i te nuinga puta i roto i nga wahine, te nuinga i muri i nga tau e wha, engari e toru tekau ētahi wā whakakitea me. I roto i nga tane syndrome tata kore e puta, me okotahi onge.

Etiology me pathogenesis

Disease Morgagni-Stewart-Morel - syndrome, pathogenesis me te etiology o e whai he whakamāramatanga kotahi. Ētahi kaituhi whakapono e he ira, me te tuku i te momo tino autosomal te māuiuitanga. He whakaaro e te tata e pā ana te syndrome ki te X-pūira. He nga take ka tukua e te mate wha nga whakatupuranga, nuinga wahine.

He take taratahi o faaiteraa syndrome i roto i nga tangata. Ko e katea ratou, a kahore e te pūtaiao ano mohiotia pehea tuku te mate kei roto i te rārangi toa. whakapono etahi e te tino maha kitea te syndrome i roto i nga wahine i roto i te menopause. Ko te raraunga putu i runga i te wā, hoatu tenei tauākī ki te pātai.

Ka taea e te mate puta tika ki mate (te nuinga Sinusitis), neuroinfections me whara roro pāmamae. I kitea Morgagni-Stewart-Morel syndrome castrates wahine nei kua i pokanga. kia kia hanga e etahi āhuatanga o te syndrome i muri i maimoatanga mate pukupuku.

He nga take, i te kitea te mate i roto i te tūroro ki te:

• myoma uterine;
• ovaries sklerokistoz;
• galactorrhea tamau;
• infantilism taihemahema.

Morgagni-Stewart-Morel syndrome: māuiuitanga

A, no te te mate, ko te kore anake nui frontal roto wheua pereti, engari matenga hyperostosis me fronto-kōpako wā kitea rohe. He maha ngā rerekētanga mōkitokito i roto i te repe endocrine. Te whakanui ake i te maha o te eosinophil me basophil ngā pūtau. Timata tini adenomatous (thyroid, uho adrenal me te t. D.).

tohu

A, no te kitea he tangata ko Morgagni-Stewart-Morel syndrome, i reira e he maha o ngā tohu e tohu ai:

• timata tūroro ki te wheako pāhoahoa auau.
• Mōmona, te nuinga i roto i te rohe puku.
• mau kiri he tae noa, engari reira maha puta pyoderma me tangi katoatia.
• I roto i te nuinga o te wā i reira ko te hypertrichosis korerotia.
• I runga i te kiri tohua pastoznost timata ki te pupuhi i te wahi o raro, puta akrozianoz.
• Uaua haaparuparu.
• He huringa i roto i te pūnaha Cardiovascular me whekau matehā (whakawhänui i te rohe ngakau, i reira he pepe turi, me te kore ngakau).
• Ko te hehema ki hinga, Tuhinga o te wahi romahā o runga, me te bronchopneumonia.
• Huringa i roto i te repe endocrine āhuatanga āhuatanga i. kia noa Exchange, nui haere te heke haere ranei.
• Heke kātakí warowaihā. E mea pinepine te mārama whakakitea mate huka.

• Ohorere huringa paheketanga. I roto i te hapūtanga, i roto i tenei wā ino roa huru o te manawanui.
• He disorders io, me te hinengaro. faaite mai ratou ia ratou i roto i te puka o te lability aronganui, kārangirangi, ohoroa me te hinaaro ki te whārua.
• Kei te maha pereti frontal hyperostosis ā-thickened wheua angaanga. I roto i ētahi wā, ara ake i te rahi o te nohoanga Turkish.

te mate

Ka taea e Morgagni-Stewart-Morel syndrome mahi i runga i te tinana i roto i ngā huarahi rerekē. E mea pinepine tei reira ki runga ki te tohu o te mōmona. Korerotia He he pānga nui i runga i te ora ngā:

• He uaua mahi o te ngakau;
• e tika ana ki te whakaeminga o te ngako puta myocardium me te pericardium;
• tūnga teitei o te HWM;
• toto tohanga, me i roto i ngā ki atherosclerosis me takawhita whakawhanake kore ngakau, i te mea he take o te hauātanga;
• ki te te manawanui ki te syndrome i atu me te mate huka, ka haamata te reira i te mate pūkoro, e arata'i ki te hekenga i roto i te tōtika kore anake, engari whakaiti hoki tümanako ora.

maimoatanga

He reira taea ki te whakakore i te syndrome o Morgagni-Stewart-Morel? Ko Treatment o te mate te nuinga i roto i te kai rite mate huka te mahi i, me te mōmona. kia waiho te kai hei iti-pūngoi, tiketike-pūmua, huaora me te kohuke tai. heke te kai te nui o te warowaihā me te ngako. whakaritea Diet Baranov te nuinga.

I tua atu, kawea te maimoatanga i roto i te mirimiri me te whakaritea ki mahi whakangungu tinana ki te whakaiti i uaua ngoikore, me te whakapai ake i tohanga piringa. Ki te he kore ngakau, te maimoatanga o te syndrome tū Diuretics kardiopreparatami me t te manawanui. D.