Hauora, Rongoā
He mate autoimmune he purapura thrombocytopenic
Hoki te wā tuatahi i te autoimmune te purapura thrombocytopenic, i whakaahuatia i roto i te 1735 Verlgofa nei kitea te mate i roto i kotahi tekau nga tau 'kotiro. I tēnei wā i raro i tenei puka ingoa ngā autoimmune thrombocytopenia, take autoaggression i ai hemo. puta ratou diathesis hemorrhagic ki hē taratahi o platelets. Tohatoha puka whakapeka, me te ma'i o te mate.
take o
Whakapeka te purapura thrombocytopenic mamae te nuinga tamariki 2 ki te 9 tau te pakeke. te purapura Thrombocytopenic i roto i ngā tamariki āhuatanga e huaki ana ohorere, me te ora tere. maha whakatairanga Whanaketanga o faaiteraa haumanu mate viral o te wahi romahā o runga wahi kūnatu ranei. I roto i te 10% o ngā take o te mate e pā ana ki te whanaketanga o te varicella huaketo, Epstein-Barr huaketo, kano, BCG immunotherapy. whakangaromanga mōtepe tika ki te whakautu ārai o te kaiao, nui atu i te mahi o te huaketo.
ka karanga momo ma'i o thrombocytopenia tonu neke atu i te 6 marama te purapura thrombocytopenic idiopathic. Ko te take o te mate, ko te unknown. maha Thrombocytopenic te purapura haamata i roto i te taiohitanga, pūhuruhurutanga. Ētahi atu noa i roto i nga wahine.
puta āta faaiteraa haumanu. Āhuatanga e te akoranga chronically-auau roa ranei o te mate. â pūtake Pathogenetic o mate te ka whakatere whakangaromanga mōtepe e autoantibodies ki a ratou.
pikitia haumanu
I runga i te kiri o te tūroro ki te tohu o te microcirculatory momo toto rite punctate ponana petechial kanokanototo subcutaneous iti, te purapura i runga i te mucosa-waha. Āhuatanga e toto o kiriuhi mucous o te ihu, ngā pae. Huringa i roto i te kiri maha e kei i runga i te mata mua o pito te kātua, runga, me te raro. Tikanga te hanganga o te toto nui i te pae i werohia. I te tahi taime i reira kia kia toto ki te teatea me te etine, toto i te wahi kūnatu. I roto i nga wahine, i reira he pakaruhanga toto i roto i te ovaries. I roto i te puka nui o te toto mate tākihi kia puta.
Ka taea e te purapura Thrombocytopenic arahi ki pōauautanga kino pērā i toto kaka , me te toto subarachnoid. Āhuatanga he pai soté whakamātautau-Konchalovsky kaingaki-LEED: hanganga o pakaruhanga toto i roto i ngā wāhanga kiri o kōpeketanga. taikiri, ate me te kōateate kore whakanuia.
tātaringa
Ko te āhuatanga matua o te taiwhanga ko ki te whakaiti i te maha o platelets. e kore e takahi wa toto upoo-. kua nui haere Heparin wē. I roto i te nuinga o te wā, i whakaritea e te hua o te immunoglobulin G platelets. I muri tino toto tautuhi anemia hemorrhagic whakapeka.
maimoatanga
Ki te pāngia ki te thrombocytopenic te purapura, timata tūroro maimoatanga ki corticosteroids. I roto i te maimoatanga, kite tūroro he hua on i roto i te mōtepe tatau tae noa ki te murunga oti. Ko te kore o te whai huatanga o corticosteroids me immunomodulators i whakaritea delagil. Ki te memeha noa o te therapy momo i roto i te 6 marama tūtohu te raveraa i splenectomy.
Ko tētahi atu wāhi o te therapy - whakahaere o pota tiketike o immunoglobulin mō te werohanga rō-uaua mō te 5 ra. Ēnei taka Tautauā paturopi e herea ka tango viral, kitakita me te tahi atu antigens.
I roto i te 80-90% o tūroro i roto i te ora noa puta i roto i 1-4 marama. I roto i ētahi wā, ka taea e te purapura thrombocytopenic muri ake ki te 12 marama. Ko te mate, ko te chronically paipa: toto wā kē ki wā o te murunga.
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