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Syndrome o CLC: āhuatanga, tohu, maimoatanga
syndrome CLC, e mohiotia ana ko te syndrome Lown-Ganong-Levine, puta i roto i te āhua 0.5% o te taupori, me ko te take o te tachycardia i 30% o te wā, he mea na reira e tika ana ki te ako ki te tātari i te aroaro o te syndrome me pehea ki te mahi ki a reira.
whakaahuatanga
Syndrome Clerk-Levy Cristescu ko te take motuhake o te syndrome o excitation taimi halá, o ventricles o te ngakau, āhuatanga nei i te mau ana i roto i te excitation ki te ventricles i runga i ara atu. whakaritea te ngakau o te tangata e kia e te ventricles roto te atria, he mea e tika ana mo te rawaka whakakī ratou ki te toto. whakaratohia Operation o tenei huarahi e te kōpuku atrioventricular, kei nei i waenganui i nga ventricles me atria, i roto i reira i reira he he pini nui pōturi e whakarato ana i te roa ki te ventricular hukihuki. Heoi, etahi iwi i te ara rerekē congenital o whakahaere te hihiko ki te hipa i te kōpuku atrioventricular, taua huarahi he paihere o Hemi, ka paihere te muka Kent Maheyma. Na roto i enei huarahi i heke te ngātere te me i reira ko te āhuatanga o CLC. Ka taea te kite i tenei tikanga te raveraa i te tātari ECG. E kore e te āhuatanga pā te mahi o te ngakau, me te e whakakitea anake i runga i te cardiogram. Ko ētahi wā i reira he take ka reira te mea he akoranga porohita o te excitation. Tenei puta ka, haere i roto i te ara anomalous, hoki te pini roto i te kōpuku atrioventricular, hurihia ranei - i muri i haere i te ara tuatahi, hoki te anomalous. tenei katoa ai te huringa i roto i te manawataki o te mokowhiti, he reira tenei tukanga huaina syndrome CLC.
Tītohunga me te syndrome CLC e congenital, he mohiotia hoki take tino o enei abnormalities. He whakaaro e te pā reira ki disorders whanaketanga o te kukune i te wā o te ngakau. Ano, e kore e whakahaere tikanga i roto i taua kia te take, me ngā ira mate.
tātari o ECG
tauturu ECG tātari ki te tautuhi i tēnei syndrome. Kei te āhuatanga i te reira i te whakaiti i roto i te PR (PQ) wā. Tenei wā tohu te wa i roto i nei tae te excitation te myocardium ventricular o te atria me te pūhui atrioventricular. I roto i te iwi pakeke atu i te 17 tau, ko te wā noa o 0.2 hēkona, engari te whakaiti o te wā, e taea meinga tachyarrhythmias, kia hoki kia he tikanga matua mō te tātaritanga o te CLC syndrome. Mai te āhuatanga syndrome āhuatanga Klerk-Levy Cristescu tītohunga Pāoa e te irava o te hihiko hongere anomalous - James kurupae honotanga marae ki te wahi distal atrioventricular o te pūhui e ai te whakaiti o te PR wā (PQ).
I tua atu ki te whakaiti i te wā i mea, te aroaro o CLC ECG syndrome kahore atu huringa. Ventricular matatini (QRS matatini - tino nui te ine i runga i cardiogram e whakaatu ana i te wahi o te excitation i roto i te ventricles) e kore e puta ohoreretia. CLC syndrome tino maha puta i roto i te iwi e kore ine tona ngakau.
tohu
He kahore faaiteraa te āhuatanga o te Manahautū-Levy Cristescu, te nuinga o te iwi ki te ara James i kore noa e mohio e pā ana ki a ratou, ka ora, kahore hūhi.
Tohu o CLC rite te syndrome ngā i roto i te huri i te auau ngakau. Tūroro i pāngia ohorere o te auau ngakau tere, e ai kia haere tahi i te bloating, whakangohe, whanoke, nge i toku matenga. I te tahi taime e taea te kite i te reira sweating me copious i mua i muri i te whakaeke ranei. He kia hoki kia pakū noa mokowhiti vitiviti.
maimoatanga
I roto i te nuinga o te wā, e kore e te syndrome CLC rapu wawaotanga motuhake. I roto i pāngia o manawanui ngakau anake e taea te aukati ia ratou ki te mirimiri motuhake, natuzhivayas wai kanohi meangiti ranei i runga i te faaururaa, e ko, e mahi ana i te nekeneke Valsalva. Ki te kore e tauturu i enei tikanga, me karanga e koe te waka tūroro.
Ano, ka pā ana ki pāngia o syndrome tachycardia meinga e te CLC, ka taea e koe te utu i nga ratonga o te mafatu, ko wai me whakarite i te rongoā motuhake, pērā i "Verapamil" ranei "Amiodarone".
I roto i te take te wahi kaha pā haurangi tachycardia te ora o te manawanui, whakahaere mahi te ki te whakangaro kurupae Hemi e ārai patunga puku porohita. e kore e mōrearea peheé ngā mahi, me muri i te manawanui hohoro haere i runga i te menemana.
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