Ectodermal me dysplasia kaiota. dysplasia tākihi

I raro i dysplasia (iritihia i Kariki rite dys - whakakāhoretanga; wplasis - mātauranga) e pā ana ki he, me te distorting te whanaketanga o tetahi okana. Ko tenei - he wā ngā uhi i tetahi maumaui.

E pā ana dysplasia kaiota ki mate o te pūnaha kōhiwi, ka e āhuatanga i roto i taua i te kiko wheua whakakapi e kiko kaiota. deforms tenei tukanga nga wheua. Ko te take matua o tenei mate ko te ahua o te tukanga puku, e haamata i te tamaiti, a ka tīmata ki te ahu whakamua. dysplasia kaiota Ko te tikanga i roto i nga wahine.

e rave rahi whakarōpū o te mate. Ko te kōwae tino noa ko, i runga i te taumata o te tini o te tukanga pathological rānei:

• monoossalnaya dysplasia kaiota pā anake kotahi wheua;
• E kitea huringa i roto i te wheua maha (te tikanga horahia i tetahi taha o te tinana, a maha puta i roto i te kōhungahunga) - poliossalnaya.

Ko te puka tuatahi o te mate pānga te wheua cranial, te mata, wheua tubular (roa) mata. Ko te tuarua - i te wa ano neke atu i te rima tekau ōrau o nga wheua katoa o te tuahiwi.

Ko te pōauautanga matua ngā piere auau, e hohoro coalesce, engari manga whakarei i roto i te wheua, me te sarcoma.

Kaiota maimoatanga dysplasia i roto i kore ara ohaoha iho, e taea e ngā tukanga orthopedic anake (transplant wheua tīwani, osteotomy), me te whakarite o te raau taero e relieves mamae.

dysplasia Ectodermal rarawhi he maha nui o mate me syndromes (e pā ana ki 100), te ngako o te mea te aroaro o te whanaketanga rerekē o pärönaki ectoderm. Ko te tohu tuatahi - te aroaro o tūāhuruiti, e ka whakahuatia, a ka patua e auau taea arahi ki te pakaru o tetahi whanaketanga hinengaro, te mate ranei.

Ka taea e koe te tīpako i te momo, me te whai ratou tohu.

haamata Angidroticheskaya ki faaite mai ano i roto i nga kohungahunga, i te tamaiti, me te haere tonu puta noa i te ora. Ko te āhuatanga matua e:

• mate tuku;
• deformation kaha o nga niho;
• te aroaro o te āta i te whao;
• atrophy mucosal (korokoro, mangai, ihu);
• Ko rite ki te tūroro tamaiti he pakewakewa congenital te ahua waho.

Te rongoā o symptomatic whakaritea. Rāhuitia: hararei i roto i nga whenua tonga, mahi i roto i ngā tipu wera me te matū.

āhuatanga Gidroticheskaya ekzodermalnaya dysplasia e huringa i roto i te kapu, kapu, te whanaketanga makawe. Ka rite ki te maimoatanga te nuinga o te wā whakahaere huaora "He" waho me roto, kirīmi tamarûraa me keratolytics. I tua atu ki tenei, te whakamahi i: te tikanga enzymatic Methyluracilum, steroids anabolic, konutea, waikawa amino me biostimulants.

dysplasia tākihi He maha ngā momo e rere:

• faaiteraa morphological (whēwhē me ohie);
• Localization (cortico-medullary, medullary me cortical);
• nuinga - katoa, segmental, rahi).

Ko te take matua o tenei mate he āhuatanga ira me te mana ā-me waho teratogenic runga kukune. Na reira, ko te pūtake o te mate he malformations congenital, e, ahakoa o te momo, arahi ki te hekenga i roto i te rahi tākihi, te whanaketanga nanakia o parenchyma, he whakaiti nui o ona mahi.

Maimoatanga o tenei mate ko take symptomatic me auau, ka reira te mea he tohu mo transplantation o te okana.

I roto i te whānui, dysplasia Kei roto he rōpū o mate e ngā whanaketanga rerekē o te okana te pūnaha katoa ranei. Ka rite ki te tikanga, te matua ai - āhuatanga ira, me te congenital.

he symptomatic Treatment, ranei he tūtohutanga mo te transplant okana wheua ranei.