Hauora, Diseases me ngā Here
Ledd Syndrome: tohu, Treatment
He huru mamae e pā ana ki te tūranga rerekē o te duodenum, te matapo, me te midgut, ka karanga syndrome Ledd. E ai ki te mea paearu whakatau te aroaro i roto i te tinana o tenei mate, me he aha ngā tikanga e ārahi i roto i tona maimoatanga - ki tenei pātai ka tūhura i tatou i roto i tenei tuhinga.
Ledd syndrome
Ko te Pākatokato o te hurihanga intestinal, i hanga nei i roto i te whanaketanga fetal (te nuinga o 10-12 wiki) me ko te kōpeketanga o te duodenum ki te na Uri cecum o te midgut, kua he ingoa etahi - Ledd syndrome.
ICD-10 - he whakarōpū noa o Tapa tātaritanga hauora whakawhanakehia e WHO. I roto i runga ki tenei Diseases Whakarōpū International whakahounga 10 pā Ledd syndrome ki mate o whēkau kūnatu (XI te piha haapiiraa). e kore e huru pathological puta atu pinepine atu i roto i te kotahi take e 500 kohungahunga me mau tamaroa taua tātaritanga ko rua ngā wā atu pinepine atu i te mau tamahine.
Kia aroha mai, kia kia hë te pakeke o te manawanui ki te taua huru mate tahi congenital, pēnei i:
- whatukuhu hypoplastic pūkahukahu ranei;
- mate ngakau;
- stenosis pūkahukahu me ētahi atu.
Ledd syndrome i roto i ngā pakeke he tino onge. kia tukuna ai intestinal te hua o te nekeneke o te cecum, me adhesions i roto i te kōhao puku. I te tahi taime i whakapataritari hanganga whaturama māuiuitanga taiepa puku he mārōrō. E kore e iti rawa i roto i te āhuatanga e pa ana i te hanganga o te kāwanatanga mate, te tākaro pukupuku Koló, me te mārere o ngā tari o te whēkau.
Tohu o te mate
Ledd syndrome i roto i whanau hou taea faaite mai tohumate iu. I tua atu ki te ruaki me te regurgitation o ate i roto i nga kohungahunga wā ai mamae i roto i te puku. I roto i ētahi wā, relapses puta, ārahi ki te whakapeka arai intestinal ki te ino, ki runga ki te collaptoid huru o te tamaiti.
tohu General o te syndrome:
- mamae paroxysmal;
- kumete whakaroa, flatulence;
- ruaki;
- huamo o te rohe epigastric ;
- retraction o nga puku o raro;
- e kore e palpation whakarato oti ngā mōhiohio e pā ana ki te huru o te manawanui.
whakaatu Radiography puku rua taumata wai i roto i te kopu, me te duodenum, a hoki he nui iti o te hau i roto i te piro. Ki te i roto i te tukanga e whakamahia ana konu pūkawa, whakaatu ana te hua te haaputuputuraa o te rerekē reo i roto i te kopu totoro me duodenum. Fakafehoanaki tenei ki nga koropiko whakanoho iho tohaina o te whēkau iti.
te tikanga heheu Ergography te warea o te cecum i te ate. Ko te whakamahi i koaro tomography computed he midgut tāutuhia huri noa iatuku mesenteric.
pikitia haumanu
Ledd syndrome - he māuiuitanga e titau wawaotanga hāparapara tonu. Ka rite ki whakahuatia mua, he iu nga tohu me taea te faahiti i wā o te maha ra, wiki ranei ara tau.
I roto i ētahi wā, e kore e hanga i te āhua mate ite ano hoki nga tau maha, me te he asymptomatic. ko te kupu mamae tamariki mate o te hiahia, kei te ërä i muri i roto i te whanaketanga ā-tinana.
I tua atu ki te syndrome puāwaitanga Ledd, te wehewehe i atu e rua puka:
- I roto i te take tuatahi kahore he koaro o te midgut, me te wāhi anomalous o te cecum, e kokopi ana te duodenum.
- I roto i te take tuarua i tawhiti anake matou midgut na Uri.
I roto i māuiuitanga (Ledd syndrome) kia whakapeka me subacute (tonu). I roto i te puka ma'i kahore e reira korerotia mamae i roto i te puku, rite colic, i ētahi wā i reira he ruaki, pohokore. He takahi o te heamana. whakaahuatia huru o te tamaiti kei te rite pai. e kore e Colon na Uri arahi ki te pakaru o ona supply toto. I roto i te uaua whēkau iti puta noa stasis toto i roto i te wahi gastrointestinal reira he huringa urupare.
Whakapeka na Uri whēkau - he tu'unga nui e i roto i te take o te rere kino ārahi ki te necrosis kikohangatia ranei o te whēkau.
Treatment o te syndrome Ledd
Te whakapai ake manawanui whānui ki ma'i-paipa akoranga mate hanga te whakamahi o āpiha antispasmodic. Heoi, ko te anake he mehua rangitahi tenei. Ko te tukanga matua i roto i te maimoatanga o te tukuna ai intestinal ko tonu pokanga. maimoatanga hāparapara o pathologies (Ledd syndrome) Kei o te maha kaupae:
- I te tīmatanga whakakorea na Uri, me te arai.
- I tua atu, ko te kōpiro iti kua he puku i roto i te tari tika, matotoru - ki te maui.
- Ki te hiahia koe ki te whakatika i nga koropiko whēkau i roto i te peritoneum kōpako, te mahi tenei whawhe. hiahiatia he mehua taua te ki he motility whēkau rerekē te manawanui.
- Whakamana te appendectomy.
I roto i nga tau tata nei, rongoā e whakamahia whānuitia tikanga laparoscopic o te tātaritanga me te maimoatanga o te syndrome. E tino whai hua pērā paku-urutomo tikanga. Heoi, wawao hāparapara i roto i te tikanga rite raro ki etahi fifi e tika ana ki te rōrahi iti o te kōhao puku, me te te matotoru iti o te taiepa puku i roto i ngā tamariki i roto i te tuatahi o nga marama o te ora. I te tahi taime i roto i te wā postoperative wawe, e ara pōauautanga:
- sepsis;
- peritonitis;
- toto intestinal;
- ileus.
Ka whakawhirinaki te tūpono o te ora tonu i runga i te putanga o te mahi. Ki te ora rohe katoa o te wahi gastrointestinal, he pai te matapae mō te taumata tiketike o te kounga o te ora. Ki te, Heoi, i reira kua nui resection intestinal, ārahi ki te syndrome o "gut poto" He raruraru ki te kai, me te pohokore te manawanui. A, no te whakamana enei hua maimoatanga hāparapara te fare ma'i, maha mo nga take o parenteral kai tōtika. I te tahi taime e haere mai te tūroro ngā mahi tukurua. Ki te whakawhanakehia ileus ki te papamuri o Simi, ki te whakahoki mai i te waitohunga kino.
faaineineraa te pokanga
Kia pāngia rite fā'ele'i tukuna ai intestinal (Ledd syndrome), kua whakawhiti te reira ki te hōhipera hāparapara, whakahaere ngongo nasogastric me te whakarato i tētahi tirotiro awakeri puku tamau. Ko te wa e hiahiatia ana ki te mahi i mehua faaineineraa te pokanga tei runga i te pakeke o te tukuna ai intestinal congenital.
Ki te whakapae i te manawanui te na Uri whēkau iti, te mahi i te mehua tātaritanga e whai ake nei:
- he whakamātautau toto mo te rōpū, me te tauwehe rH;
- he whakamātautau toto mo ngā taumata o te pūtoto, me te hematocrit;
- tātari i runga i coagulation toto.
I roto i te take o te ileus iti taea te tango i te faaineineraa te pokanga ake ki te 24 haora. I roto i tenei wa atu te korenga i te hou ki te tirohanga ki te tāutu taea o comorbidities. Ko te kupu whakahaere waikeri pekitīlia, ngā te nui o tini tohaina whakaritea e whaowhia therapy, paturopi me āpiha hemostatic. ture kai kōhungahunga.
Nuinga o ngā tamariki i roto i te wā postoperative noho ventilation aunoa auroa, e kia muri ake ki nga ra e rima. whakamahi therapy paturopi taero kaha ki huakita hāorakore. aroturuki Microecological tūnga i te iti rawa e rua i te wiki. E rua tekau-wha haora i muri i te pokanga ki rongoā ki te whakapai ake i motility intestinal, me te biologics.
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