HauoraDiseases me ngā Here

Ledd Syndrome: tohu, Treatment

He huru mamae e pā ana ki te tūranga rerekē o te duodenum, te matapo, me te midgut, ka karanga syndrome Ledd. E ai ki te mea paearu whakatau te aroaro i roto i te tinana o tenei mate, me he aha ngā tikanga e ārahi i roto i tona maimoatanga - ki tenei pātai ka tūhura i tatou i roto i tenei tuhinga.

Ledd syndrome

Ko te Pākatokato o te hurihanga intestinal, i hanga nei i roto i te whanaketanga fetal (te nuinga o 10-12 wiki) me ko te kōpeketanga o te duodenum ki te na Uri cecum o te midgut, kua he ingoa etahi - Ledd syndrome.

ICD-10 - he whakarōpū noa o Tapa tātaritanga hauora whakawhanakehia e WHO. I roto i runga ki tenei Diseases Whakarōpū International whakahounga 10 pā Ledd syndrome ki mate o whēkau kūnatu (XI te piha haapiiraa). e kore e huru pathological puta atu pinepine atu i roto i te kotahi take e 500 kohungahunga me mau tamaroa taua tātaritanga ko rua ngā wā atu pinepine atu i te mau tamahine.

Tikanga, whakapumautia te tātaritanga te i roto i te wiki tuatahi o te ora, he manawanui iti, he iti iti - i roto i o te ora tuatahi te marama. Hei kawe i te tātaritanga tika i te tākuta tamariki titau wheako me te whānui taunga ki te mate. I roto i tenei whakaaro, e kore e kitea tonu te mate i roto i te wā. Kei te ruaki i te tohu tino kitea o te mate i roto i nga ra tuatahi o te ora ate.

Kia aroha mai, kia kia hë te pakeke o te manawanui ki te taua huru mate tahi congenital, pēnei i:

  • whatukuhu hypoplastic pūkahukahu ranei;
  • mate ngakau;
  • stenosis pūkahukahu me ētahi atu.

Ledd syndrome i roto i ngā pakeke he tino onge. kia tukuna ai intestinal te hua o te nekeneke o te cecum, me adhesions i roto i te kōhao puku. I te tahi taime i whakapataritari hanganga whaturama māuiuitanga taiepa puku he mārōrō. E kore e iti rawa i roto i te āhuatanga e pa ana i te hanganga o te kāwanatanga mate, te tākaro pukupuku Koló, me te mārere o ngā tari o te whēkau.

Tohu o te mate

Ledd syndrome i roto i whanau hou taea faaite mai tohumate iu. I tua atu ki te ruaki me te regurgitation o ate i roto i nga kohungahunga wā ai mamae i roto i te puku. I roto i ētahi wā, relapses puta, ārahi ki te whakapeka arai intestinal ki te ino, ki runga ki te collaptoid huru o te tamaiti.

tohu General o te syndrome:

  • mamae paroxysmal;
  • kumete whakaroa, flatulence;
  • ruaki;
  • huamo o te rohe epigastric ;
  • retraction o nga puku o raro;
  • e kore e palpation whakarato oti ngā mōhiohio e pā ana ki te huru o te manawanui.

whakaatu Radiography puku rua taumata wai i roto i te kopu, me te duodenum, a hoki he nui iti o te hau i roto i te piro. Ki te i roto i te tukanga e whakamahia ana konu pūkawa, whakaatu ana te hua te haaputuputuraa o te rerekē reo i roto i te kopu totoro me duodenum. Fakafehoanaki tenei ki nga koropiko whakanoho iho tohaina o te whēkau iti.

te tikanga heheu Ergography te warea o te cecum i te ate. Ko te whakamahi i koaro tomography computed he midgut tāutuhia huri noa iatuku mesenteric.

pikitia haumanu

Ledd syndrome - he māuiuitanga e titau wawaotanga hāparapara tonu. Ka rite ki whakahuatia mua, he iu nga tohu me taea te faahiti i wā o te maha ra, wiki ranei ara tau.

I roto i ētahi wā, e kore e hanga i te āhua mate ite ano hoki nga tau maha, me te he asymptomatic. ko te kupu mamae tamariki mate o te hiahia, kei te ërä i muri i roto i te whanaketanga ā-tinana.

I tua atu ki te syndrome puāwaitanga Ledd, te wehewehe i atu e rua puka:

  1. I roto i te take tuatahi kahore he koaro o te midgut, me te wāhi anomalous o te cecum, e kokopi ana te duodenum.
  2. I roto i te take tuarua i tawhiti anake matou midgut na Uri.

I roto i māuiuitanga (Ledd syndrome) kia whakapeka me subacute (tonu). I roto i te puka ma'i kahore e reira korerotia mamae i roto i te puku, rite colic, i ētahi wā i reira he ruaki, pohokore. He takahi o te heamana. whakaahuatia huru o te tamaiti kei te rite pai. e kore e Colon na Uri arahi ki te pakaru o ona supply toto. I roto i te uaua whēkau iti puta noa stasis toto i roto i te wahi gastrointestinal reira he huringa urupare.

Whakapeka na Uri whēkau - he tu'unga nui e i roto i te take o te rere kino ārahi ki te necrosis kikohangatia ranei o te whēkau.

Treatment o te syndrome Ledd

Te whakapai ake manawanui whānui ki ma'i-paipa akoranga mate hanga te whakamahi o āpiha antispasmodic. Heoi, ko te anake he mehua rangitahi tenei. Ko te tukanga matua i roto i te maimoatanga o te tukuna ai intestinal ko tonu pokanga. maimoatanga hāparapara o pathologies (Ledd syndrome) Kei o te maha kaupae:

  1. I te tīmatanga whakakorea na Uri, me te arai.
  2. I tua atu, ko te kōpiro iti kua he puku i roto i te tari tika, matotoru - ki te maui.
  3. Ki te hiahia koe ki te whakatika i nga koropiko whēkau i roto i te peritoneum kōpako, te mahi tenei whawhe. hiahiatia he mehua taua te ki he motility whēkau rerekē te manawanui.
  4. Whakamana te appendectomy.

I roto i nga tau tata nei, rongoā e whakamahia whānuitia tikanga laparoscopic o te tātaritanga me te maimoatanga o te syndrome. E tino whai hua pērā paku-urutomo tikanga. Heoi, wawao hāparapara i roto i te tikanga rite raro ki etahi fifi e tika ana ki te rōrahi iti o te kōhao puku, me te te matotoru iti o te taiepa puku i roto i ngā tamariki i roto i te tuatahi o nga marama o te ora. I te tahi taime i roto i te wā postoperative wawe, e ara pōauautanga:

  • sepsis;
  • peritonitis;
  • toto intestinal;
  • ileus.

Ka whakawhirinaki te tūpono o te ora tonu i runga i te putanga o te mahi. Ki te ora rohe katoa o te wahi gastrointestinal, he pai te matapae mō te taumata tiketike o te kounga o te ora. Ki te, Heoi, i reira kua nui resection intestinal, ārahi ki te syndrome o "gut poto" He raruraru ki te kai, me te pohokore te manawanui. A, no te whakamana enei hua maimoatanga hāparapara te fare ma'i, maha mo nga take o parenteral kai tōtika. I te tahi taime e haere mai te tūroro ngā mahi tukurua. Ki te whakawhanakehia ileus ki te papamuri o Simi, ki te whakahoki mai i te waitohunga kino.

faaineineraa te pokanga

Kia pāngia rite fā'ele'i tukuna ai intestinal (Ledd syndrome), kua whakawhiti te reira ki te hōhipera hāparapara, whakahaere ngongo nasogastric me te whakarato i tētahi tirotiro awakeri puku tamau. Ko te wa e hiahiatia ana ki te mahi i mehua faaineineraa te pokanga tei runga i te pakeke o te tukuna ai intestinal congenital.

Ki te whakapae i te manawanui te na Uri whēkau iti, te mahi i te mehua tātaritanga e whai ake nei:

  • he whakamātautau toto mo te rōpū, me te tauwehe rH;
  • he whakamātautau toto mo ngā taumata o te pūtoto, me te hematocrit;
  • tātari i runga i coagulation toto.

whakamana maimoatanga hāparapara te i runga i te pütake ohotata, te faaineineraa te pokanga e te mōrahi o te kotahi haora. Ko te tamaiti kawea therapy whaowhia, hemostatics whakahaere, Pë, i ētahi wā ventilation. Kei te whakaurua e te pū tōngāmimi ki te rua pokapū.

I roto i te take o te ileus iti taea te tango i te faaineineraa te pokanga ake ki te 24 haora. I roto i tenei wa atu te korenga i te hou ki te tirohanga ki te tāutu taea o comorbidities. Ko te kupu whakahaere waikeri pekitīlia, ngā te nui o tini tohaina whakaritea e whaowhia therapy, paturopi me āpiha hemostatic. ture kai kōhungahunga.

Nuinga o ngā tamariki i roto i te wā postoperative noho ventilation aunoa auroa, e kia muri ake ki nga ra e rima. whakamahi therapy paturopi taero kaha ki huakita hāorakore. aroturuki Microecological tūnga i te iti rawa e rua i te wiki. E rua tekau-wha haora i muri i te pokanga ki rongoā ki te whakapai ake i motility intestinal, me te biologics.

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