Hauora, Diseases me ngā Here
Lefgrena syndrome: Take, āhuatanga haumanu, maimoatanga, te ārai
Kua tonu kua mate pūnahanaha te mea ngaro ki te ao hauora. Ko tētahi he sarcoidosis, e kore i nei i tika ai te etiology me whakaaturia i roto i te puka o te mumura o te kiko tūhonohono i roto i ngā whēkau me te kopa ki te hanganga o granulomas. Lefgrena syndrome - he motuhake mō te sarcoidosis e pā te kiri, taikiri intrasternal me hononga.
take o
Ko te pathogenesis Ko te whanaketanga o te whakautu autoimmune. Ko te tukinga pūnaha ārai mate, me ma pūtau toto timata ki te patu i te hauora pūtau pūkahukahu, hononga, me te kiri.
maha whakawhanake Lefgrena syndrome i roto i taitamariki wahine (20-35 tau). Tamariki te tikanga e kore ratou e whiwhi mate. tīmata te ume nei Lefgrena syndrome, a ka āta te mau faaiteraa haumanu kia tango ratou wahi. E mea pinepine, i reira te mea he akoranga pai o te mate.
Haunga ariā viral me kitakita o te whanaketanga o te sarcoidosis, i reira he ano te whakapono e whakawhanake te mate i roto i te iwi i te wa roa i roto i te whakapā ki matū ahua i roto i wheketere. kia kore e ngaro koe titiro o, me te take tuku. Ko e 'uhinga sarcoidosis polyetiological ko te mate autoimmune.
faaiteraa haumanu
Lefgrena syndrome i roto i te sarcoidosis faaite polisimptomno. timata te ume nei faaiteraa haumanu. Ko te tangata e erythema nodosum i runga i te tinana, te mea he fakahehema ki horapa ki nga topito, hoki, puku me te kaki. Kōpuku i te āhua porotītaha, kia tae ratou diameter ake ki 6 henimita. Me kï reira e i roto i te wahi o te hanganga o te erythema kore e puta necrosis.
whakaaro te faaiteraa matua te ki te waiho i te mate o te arahau me tracheal repe. tohu tenei he ati nui mo te manawanui:
- he mare;
- wā nui haere te pāmahana te tinana;
- taumaha hauora;
- reira he sweats po;
- taumaha te kounga o te moe;
- puta te ngaronga taimaha;
- wheako manukanuka te tangata.
I muri mai te āhuatanga Lefgrena syndrome e pāpaka o te hononga iho. riro ratou mamae edematous me ino nekeneke. Tautika, ka taea e tetahi mōhio te puku o te taikiri i roto i te kaki, me te i roto i te peke.
Me pēhea te ki te tātari?
whakapumautia Lefgrena syndrome te i runga i te pūtake o tātaritanga taiwhanga me whakamātautau o kaihaumanu o te manawanui. nui nui i roto i Tātaritia tenei puka o sarcoidosis Erythema nodosum. Heoi, me te kitea i te tākuta i te mate kohi mau ma'i dermatovenereological ranei.
ka whakaatu whakamātautau toto Laboratory:
- ake i roto i ESR;
- leukocytosis;
- te ahua o te kama globulin.
I te X-ray e taea te kite i te whakapakoko i te āhuatanga taikiri rahi, me te putunga kaiota te. E āwhina ana tēnei ki te kia tino i roto i te take o te mate pūkahukahu.
Ngonge whakahuatia i roto i te puka titau te bronchoscopy ki unuhanga. A, no te kore e taea e te kite i te ako o te pūkahukahu kikokiko te hanganga histological āhuatanga o sarcoidosis: kimi huānga granulomas epithelioid.
Waitohunga me pōauautanga o te mate
Takitahi rere Lefgrena syndrome. Kia pehea te roa, me te aha e kia whakautu anake te matapae ki etahi paearu. Kei te mohiotia te reira e te tuakana te tangata, te waitohunga rawakore. Ki te kore koe e tono i roto i te wa ki te kite i te tākuta, i whakaroa te syndrome te me te piri ia e te pōauautanga:
- tukuna ai arahau;
- iti hoki romahā;
- te whanaketanga o "ngakau pūkahukahu";
- emphysema;
- he tipu kitakita.
kore Respiratory whanake i muri i tukuna ai arahau. Kei te āta huru o te manawanui rite timata nga pūkahukahu ki te whakakapi i te kiko tūhonohono, kia mutu te tukanga māhorahora i muri i 1-2 tau hōloa.
Ina e, ka tīmata te ngakau ki te whakapiki ake i tika ki te kore o te hāora i roto i te toto. Otiia e kore e ti'a ia tatou ia tau'a ore i te tono mo te tauturu a te taote, no te mea he treatable inaianei Lefgrena syndrome.
maimoatanga
Kia aroha mai, e kore MEDCO taea tino whakaora sarcoidosis, mai kore e mohiotia tino tona etiology. Ko tākuta whakahau therapy motuhake e he taea ki te mutu i te tukanga whanaketanga, aroturuki Lefgrena syndrome. haamata Maimoatanga ki te ūnga steroidal drugs anti-inflammatory mō te mate iti. whakaritea hoki complexes huaora, antioxidants, immunosuppressants.
Ko te akoranga o te maimoatanga pumau te toharite o 8 marama. Te reira i katoa tei runga i te āhuatanga takitahi o te pūnaha ārai mate. Kaiwhakamana whakahauanga Taki-ake hauora mo te pulmunologom rata mate, tano pumau reira 5 tau.
He aha te mea te ārai?
Kia kore ai te whanaketanga o te sarcoidosis, kia tango te tuatahi tiaki o ratou ara o te ora. kia kai taurite, Kei roto te ngako, pūmua, te warowaihā i roto i te ōwehenga tino arotau.
Iwi aro ki sarcoidosis, kia hoatu ake kai paipa, te whakapā ki te matū matū pukuriri.
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