HauoraDiseases me ngā Here

Nahea raruraru myasthenic? maimoatanga

Tetahi raruraru - ko reira te huru tangata, i roto i nei ohorere, tere taumaha akoranga o te mate, te tohu o piki te ora-te whakawehi rawa hohoro. Myasthenic me cholinergic raruraru, ko te hoa o te myasthenia gravis, e kino hoki kia ngaro te manawanui manawa, ka mutu tona ngakau te patu. I te tahi taime te ora o te tangata kiia mau meneti, e kia whai iwi hauora tata ranei te tika ki te whai wa ki te āwhina i. He aha te na te ähua, e mea he kore te mea, gravis he myasthenia mate whakamate? whakahere tatou he reo mahinongofua ohie ki te korerotia ki te tangata e pā ana ki te mea e mohio katoa: nga take o te raruraru myasthenic me cholinergic, whare hauora, whawhati tata tiaki ki te hunga ki nei tupu taua raruraru. Pea te tangata kati ki a tatou, ki te ohorere i roto i te waka ranei noa i runga i te huarahi, ka waiho reira kino, te mōhiohio i roto i tenei tuhinga ka āwhina i whakaora ora.

myasthenia

Ko te kōrero e pā ana ki te Stroke tīmatanga mā te whakamārama i te ariā o te myasthenia gravis. I te tahi taime tango a tawhio noa tenei mate i waho te rohe utu, rite te mamae i myasthenia tonu amuamu o rohirohi, lethargy, taea ki te mahi i tetahi mahi tinana, tika te māmā. I roto i te meka, gravis myasthenia te he mate uauaio, e pā ana ki te kāwai o te autoimmune, meinga e te e te kore i roto i te tinana hua nga he paturopi tika hanga o ngā pūtau ōka e patu i te kopa hauora me ngā pūtau e riro te raruraru nui ranei.

whakawhanake raruraru Myasthenic i runga i te whakamārama o te mate whānui, me he rite tohu ki a ia, faaite mai ratou anake ki te whānuitanga nui nui e arahina mua ki te mate o āhua 40% o tūroro. Na, ki te tīmata te maimoatanga te tere, te mate e taea te karohia. hiahia ana ahau ki te mōhio i taua myasthenia mate 10 iwi i roto i nga 100 mano tangata o te whenua, me nga wahine kua pāngia e te reira 3 ngā wā atu pinepine atu i te tangata. gravis Myasthenia taea whakaatu ano i roto i te tamarikitanga, engari he onge ngā take pēnei i. Kei te nuinga kitea te reira i roto i tūroro i te 20 tau, me te ki runga ki te koroheketanga.

Ko te tohu o te myasthenia gravis

Te kore gravis myasthenia, ki te he te reira reira tangata i roto i, raruraru myasthenic taea kore puta. Heoi, i te tahi taime tango reira i runga i etahi atu mate ki tohu rite, hei tauira, pērā i te faahitihia lethargy, ngoikore, te rohirohi. tohu atu i roto i nga kohungahunga:

- Hawaiki kamo, tino kitea i roto i te ahiahi, me te heke i roto i te ata i muri i era atu o te po;

- kite rua;

- pau, i muri i pikaunga rohirohi tiketike tikanga mo te tahi atu iwi, pērā i piki i te pikitanga;

- tohu bulbar tuatahi (ahua nasal reo i muri i te kai, me te korero roa, uaua i roto i te whakahua o reta takitahi);

- akiaki tohu bulbar (uaua i roto i te horomia, rāoa auau);

- pōrearea autonomic (paresis intestinal, tachycardia);

- ngā āhuatanga kanohi (i runga i te rae kita hohonu rawa, āhuatanga mata);

- salivation nui;

- uauatanga i roto i pupuri i te matenga;

- uaua i roto i te haere.

He āhuatanga motuhake o te myasthenia - katoa o nga tohu i runga ake he kino i muri kohakoha tinana, me te i roto i te ahiahi, me muri i te okiokinga pai e iti rawa ngaro ranei.

Tohutanga o raruraru myasthenic

Ki te mamae tetahi tangata i myasthenia gravis, i raro i etahi huru, kia waiho ai hei raruraru myasthenic. Ko te tohu o te mate e whāriki ana, rawa pērā i tachycardia, rohirohi tiketike uaua faufaa (romahā, cardiac), salivation, i te wa ano whakakaha. He angamaheni mo te raruraru i te āhuatanga e whai ake nei:

- pāpāngia o nga uaua o horomia me te reo, kia taea te tiki e ki te wahi romahā hūpē, huware, kai;

- kiha;

- rōpū, kaha, me te whakaoho tika ki te kore o te rangi;

- he werawera makariri;

- urination ētahi wā māhorahora defecation me / ranei;

- mate o te mahara;

- kiri maroke;

- hūpeke pēhanga toto;

- tamariki dilated;

- kore ngakau whakapeka, e ko te takahi o te ngakau.

Ko raruraru Myasthenic o te maha nekehanga:

- ngāwari;

- toharite;

- taimaha;

- uira.

takoto te rerekētanga i roto i te mau faaiteraa mana i runga tohumate. Rawa uira mōrearea me te raruraru taimaha i roto i nei i te tangata rawa hohoro, i roto i o meneti tika te tokorua, whakawhanake ngoikore o nga uaua romahā me te horomia. riro tere i te tuatahi manawa, fehangahangai whero, mokowhiti ake te pēhanga, auau ngakau tae e pā ana ki 160 kapakapa ki te meneti. Na ka tīmata te manawa ki te kia haukotia, a kia ngaro rawatia e, tona mata tahuri puru (i roto i te rongoā huaina te mea cyanosis), heke te pēhanga, he pini papaki ana nga korero.

Take o te raruraru myasthenic

Ka taea e Myasthenia gravis e congenital riro ranei. meinga ana te tuatahi e te irakētanga i roto i te ira. whakawhanake te tuarua, ka kua he tangata:

- raruraru ki te repe thymus;

- te tahi mau puka o mate pukupuku (hei tauira, uma, pūkahukahu, ovaries);

- hyperthyroidism;

- encephalitis lethargic.

Ki te whakamārama o enei mate e taea raruraru myasthenic puta i roto i te wā e whai ake nei:

- mate hopuhopu whakapeka, tae atu te mahaha, rewharewha, Bronchitis;

- mahi;

- te ahotea hinengaro kaha;

- mahi tinana High;

- tango etahi rongoā (hei tauira, tranquilizers);

- disorders hormonal;

- haere myasthenia tūroro tango nga pire, te tūkino o te akoranga maimoatanga.

raruraru cholinergic

maha puta raruraru Myasthenic me cholinergic i whakarara, i te mea he aha i reira he hapa i roto i te pārōnaki me, rite te hopearaa o te maimoatanga. Heoi, enei e rua ahua rite faaiteraa waho o te kāwanatanga meinga e take rerekē, me te whai etiology rerekē.

Ko te kupu, ina heke myasthenic receptors raruraru cholinergic te kiato o te membrane tika ki to ratou whakangaromanga, me te toe whakaputa ke ratou mahi. puta te raruraru cholinergic faaitoitoraa ka nui o receptors cholinergic (o te nicotinic me / ranei muscarinic). Rere te tukanga fariiraa o teuteu mo te maimoatanga o te myasthenia gravis i pota tiketike, me te tikanga e kua rāhuitia i roto i tenei mate.

e kore te mea ngāwari tātari te raruraru, no te mea hāngai ona tohu matua ki myasthenic. Āwhina tika te whakatau he aha ka tūpono ki te tangata, kia waiho he āhuatanga taua tona huru, āhuatanga o te raruraru cholinergic: E whakaatu ana te manawanui tohu o te haurangi: mamae puku, oroko ruaki, tīmata korere. Hoki raruraru myasthenic āhuatanga e katoa anake aua tohu.

Ko te āhuatanga tuarua ko te raruraru cholinergic - ähua tohu o myasthenia gravis kahore te raveraa i ngā mahi tinana, engari i muri i tango taero cholinesterase.

raruraru whakauru

Ko te reira i te momo hauora me te ora kino o te māuiuitanga. fakatahai te reira i raruraru myasthenic me cholinergic, e whakaatu ana kua korerotia kotahi tikanga katoa ki te tohu e rua. tēnei, he uaua ki te fakatonutonu tātaritanga, engari ake ara - maimoatanga, no te mea te hunga rongoā e whakaora i te raruraru myasthenic, cholinergic whakahōhā atu. A, no te nga mōrearea rere whakauru wehewehe rua ngā wāhanga:

1. myasthenic. E kitea tūroro disorders bulbar korerotia, raruraru romahā, mahi tinana ai rohirohi, engari te whakahaere o te raau taero ( "Klamin", "Neostigmine") e kore e meinga tauhohe kino.

2. Cholinergic āhuatanga e tohu o te haurangi.

whakaaturia Practice kua e te tupu pinepine mōrearea whakauru i roto i te iwi nei i tangohia kē ake tenei ranei e raruraru i roto i nga kohungahunga.

Ka taea e kia parenga raruraru whakauru o taua mau faaiteraa āhuatanga:

- tūroro mārama kitea uaua te kupukupu tonu ke iti me bulbar ofatiraa me nekeneke mahi o wahi;

- e kore e fuoloa ki tango rongoā whakaiti tohu pathological, pērā i pai ake mahi nekeneke, me te whakauaua āwhina ū manawa.

tātaringa

Ki te karo i hape, me te hohoro hoatu tokoni hua i roto i te raruraru myasthenic, he mea nui ki te hoatu i te tātaritanga ki te manawanui tika. Ka rite ki tuhia i runga ake, kia waiho etahi tohu reira raruraru myasthenic i roto i mate e kore e pā ana ki te myasthenia gravis (hei tauira, te uaua manawa, mokowhiti kōhikohiko). Tohutanga raruraru cholinergic rite ki taua ite i roto i haurangi, me etahi raruraru ki te wahi kūnatu. Ki te mea he kaiwhakamau, taea ki te hoatu mōhiohio e pā ana ki te aroaro o tona myasthenia me rongoa ki te tango i a ratou i te manawanui, te nui faingofua tātaritanga ōkawa. Ki te rerekëtanga i te momo o te raruraru, tākuta mahi prozerinovuyu tauira.

E kitea uaua Special o tātaritanga i te Stroke whakauru. I roto i te tikanga ki te whakatau i tona te wāhanga tuatahi hapa-free kawea i roto i te tātari haumanu o te manawanui, me te aromatawai electrophysiological o te pānga i whiwhi e te fariiraa i anticholinesterase taero.

Ko te aroaro rawa o te tangata gravis (i mua i te raruraru) kitea e te tikanga o te electromyography, computed Tomography, pharmacological me ngā whakamātautau immunological.

tiaki Emergency i roto i te raruraru myasthenic me cholinergic

Ki te he manawanui ki te myasthenia kitea rawatia ake tupuheke (mai raruraru), i te ora haere i runga i te meneti. Ko te mea matua e Me mahi a tawhio noa - karanga tonu te waka tūroro. Kia aroha mai, i roto i to tatou mo'oni, i reira he wā ka roa tiaki motuhake te. Nahea tatou e nehenehe e tauturu i te mate i roto i te take taua? Tuatahi, ngana ki te whakarato ia ki te manawa, te tango i nga hūpē i tona korokoro. E ai ki nga ture, me te mate ana i te myasthenia kia whai koe i te tuhipoka o ki te whai ratou i te mate, me taero (pērā i "Neostigmine") me te pūwero. Ki te kahore he taenga tere wawe tonu, he tangata ki te raruraru myasthenic he tika ki te hanga i te werohanga rite ki te kōrero i roto i te tuhipoka.

Ka tae ki te whakaora, e hiahiatia tākuta ki te hospitalize te manawanui i roto i te mea o te ru, me te i roto i te kōwae tiaki kaha, te wahi i te kaha maimoatanga whawhati tata:

- te whakarato i tētahi airway;

- supply o te hāora;

- pūmārō me te ventilation aunoa.

Ki te kahore he tohu o te raruraru cholinergic (ruaki, korere) te manawanui, whakaurua nga rongoa e whai ake nei: "Neostigmine", "Atropine". I roto i te aroaro o ngā tohu o te haurangi maimoatanga whawhati tata he mea anake i roto i te ventilator me i te werohanga o enei raau taero, "Atropine", "immunoglobulin", me te etahi atu whakaaro hauora ka tohua.

maimoatanga

Ki te i te tangata, he raruraru myasthenic, maimoatanga i muri i maimoatanga ohorere kawea atu ki runga ki te pūtake o whakamātautau haumanu me te taiwhanga, me tātari te akiaki o te mate. Ka taea te kawea ventilation Mechanical (arā, ventilation tāwhaiwhai o nga pūkahukahu), i runga i te huru haumanu o te manawanui, me te te whakaaturanga o te aroaro o te hāora i roto i te toto rānei i runga ki te ono nga ra, engari ki te te manawanui i muri i te 16 kia ranei haora, neke atu rānei i reira ko te tauhohenga pai ki "Neostigmine" takahi ventilator . Ko te tikanga, ko te tikanga he ventilator rawa taumaha, me te aro, tono haere tonu te aroturuki o respirators,% i roto i te hanganga o ngā haurehu toto, tohanga toto, te pāmahana, kūtere toenga i roto i te tinana, me etahi atu.

He tikanga pai ki te akakoromaki i nga mea katoa o mōrearea i roto i nga kohungahunga, ko te plasmapheresis utu. A, no te kawea tenei tīpako toto i roto i te pokapū (whatīanga ranei) rua, centrifuged, te huringa i roto i te kaituku wē tāwhaiwhai ranei. Tenei tikanga homai hua pai - i roto i te nui ake o haora o huru o te manawanui he tokorua. whakamana Plasmapheresis te i te akoranga 7 ki te 14 nga ra.

Ko tētahi o nga wāhanga o te maimoatanga he therapy tarukino. E ai ki te whakaaturanga o te tūroro pēnei ki immunoglobulins, antioxidants, taero anticholinesterase, a i roto i te aroaro o te mumura - paturopi.

Matapae me te ārai

E toru tekau e wha tekau ranei tau ki muri, kua puta rawa pinepine putanga mate i roto i te tūroro ki te myasthenia i roto i exacerbation o te mate. Na kua te auau te tahuti nei kua heke e 12 ngā wā. whai ki te matau e te tahi mau taime i ta tatou mau ohipa ki a koutou tei runga i te ora o te tangata, i a te raruraru myasthenic koe. kia āwhina Emergency kia whakaratohia rawa hohoro. Na reira, ki te ohorere i runga i te huarahi, i roto i te waka tūmatanui, nga wahi katoa e kite tatou i te tangata e tīmata ana ki te kowaowaotia, e hiahia ana koe ki te karanga i te waka tūroro tonu.

Me ū hoki tūroro Myasthenia ratou ki te maha o mehua ki te ārai i te raruraru:

- kia i raro i te tirotiro o te tākuta, a tino ū ki te maimoatanga whakatakotoria;

- A ape i te māuiui, breakdowns io;

- taea kaitiaki ki ngā mate hopuhopu;

- e kore e maka atu koutou haurangi tinana;

- i roto i te kai ki te ngā kai taonga i roto i te pāhare pāporo (hei tauira, rihi rīwai, karepe).

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