He aha te mea te syndrome Kalman? a Kallman Syndrome: tohutanga, te tātaritanga me te maimoatanga o ngā

"Ofatiraa" Ka taea e te ira kotahi arahi ki mate rawa nui, te rongoa ratou rawa taea. Ko tētahi o ēnei pathologies he syndrome o Kallman. puta te nuinga o tenei syndrome i roto i nga tangata, ahakoa i ētahi wā e kitea rawa māngai wahine reira.

whakaahuatanga General o te mate

syndrome o Kallman - te pīari iranga tuku nei te rite te autosomal ngoikore, autosomal tino me te X-hono ira.

disorders mate te āhuatanga o te hypothalamus me repe. Ai te tuatahi hē hua tuku tauwehe. Ia, i roto i te tahuri, āwhina ana ki te whakaiti i te hanga o gonadotropin i te repe. Ko te mahi noa o gonads te kupu riro taea.

Ko te take o te whanaketanga mate

Kallman syndrome - he mate iranga e taea te pōreareatanga i tetahi mea. Ko te take tuatahi o te mate ko te hononga he o ngā pūtau tane, he wahine i te wa o te haputanga. Ko, i tetahi o nga pūtau me roto i te "whati" ira e homai he tūponotanga nui o atu faaiteraa o te mate i roto i ngā tamariki.

Noatia, e taea te pāngia te ino o te kounga ira o te pata i ngā āhuatanga o waho. Ko te matua o ratou ko te āhuatanga taiao. kia meinga hoki te rongo auroa ki ngā matū ngā irakētanga. Ka taea e Kallman syndrome faaite mai ano rawa mārama whakahuatia i roto i, ine iti i te täkupu ranei.

tohutanga o te mate

Kanohi e te mate he tohu motuhake, pera he reira ngāwari taiea i te tahi atu pathologies. Ki te kitea he manawanui te syndrome o Kallman, kia ngā tohumate:

• pūhuruhurutanga oti. I te tahi taime te mea tata rawa ngaro. Hei tauira, tohu tangata i te nui iti o te testicular - 3 anake ml (tikanga kia waiho reira 12 mL).
• ähua Hyperplastic me ngoikore o te Tunaroa.
• He hypoplasia tohua o te ure me te repe repeure.
• Tohatoha o te kiko adipose rite te wahine.
• ngaro tonu te kanohi ranei o āhuatanga fakasekisualé tuarua. Hei tauira, nga tangata kia ngaro ai huruhuru i runga i te tinana.
• passivity Fakasekisualé.
• malformations Pūnaha: ngao ngatata, ngutu ngatata, rangi Gothic.
• Ngoikore ki te kite kakara. Ko te kupu pangia e tonu perception.

kia faaite ēnei tohumate kia tino ngoikore ranei. Te reira i katoa tei runga i te tohu o te pīari i roto i te hypothalamus me rapae o.

tātaritanga Āhuatanga

e kore te mea he mate rawa noa Kallman syndrome (whakaahua o tūroro tukuna ki te rauemi motuhake o ngā kaupapa hauora, whakaatu mārama rerekētanga i roto i te hanganga o te tinana tane). Heoi, ki te hamani tona tātaritanga kia tokanga makehe. E whakarato ana i mo te whakatinanatanga o taua mahi:

1. Taki nga taumata taketake o hormones i te tinana: estradiol, testosterone, prolactin, tupu taiki. Whakamātau roa, me te tohu. Kei te tū te reira i te iti rawa i te wiki.
2. ka tauturu i te rangahau atu tohunga te wehe i te syndrome i roa kaupapa ture whanaketanga fakasekisualé.
3. Tirohia tūtohutanga ki kakara. meatia tenei te matū rawa noa, i homai te manawanui kei (hopi, kakara), me te kakara kaha. E ai ki te rangahau mutunga: tikanga noa o te kakara i roto i te tangata e kore e ranei.
4. US täkihi me te raho.
5. MRI o te rapae o me hypothalamus. I tua atu, i roto i te tomograph whakamātautau he e tika ana ki te whakarongo ki tetahi pukupuku i te matenga e taea meinga te ahua o nga tohu whakaahuatia ana i runga.
6. Kohikohi i te aamu utuafare. Mai riro te māuiuitanga aroaro te, whiwhi mōhiohio e pā ana ki ngā take o te mate i roto i te utuafare o te manawanui ka meinga e taea ki te whakaora i te tātaritanga tika tino.

Āhuatanga o te maimoatanga

Mai te mea ira te mate, ka too atu o reira e kore e waiho e taea. Heoi, me kia kawea maimoatanga ki waho. i muri tonu i te tātaritanga, faaterehia te manawanui te testosterone. meatia te hātepe kei te i roto i te marama torutoru.

Nā ki taea taua ngaio therapy whakatutuki i te whakapai ake i roto i te āhua whānui o te manawanui o te hauora, te whakarei ake hiahia fakasekisualé. I tua atu, verilizatsiya tutuki. I muri iho, haere tonu kaiwhakaako therapy, e hāngai ana ki te whakaora i te taea o te whakatupuranga o te parāoa pakeke. I roto i tenei take, e kore tono testosterone me gonadotropins.

Kia mōhio ki te kua te tangata kua pāngia ki "syndrome Kalman", ka whai i te maimoatanga ki te whakahaere i te ora. Ka whai wāhi te reira ki te tiaki o ngā āhuatanga fakasekisualé tuarua, me te faaho'iraa mai o te ora ngā noa. Heoi, ki te mea te manawanui ki tenei tātaritanga ka maia ki te whai tamariki, kia kōrero tonu ratou i te iranga. tonu tiketike rawa te mōrea o ia i te tamaiti ki te māuiuitanga rite. I roto i te toenga - ki te iti o ngā tohu, me te maimoatanga tika - te manawanui e taea arahi i te ora rawa noa.

Ki te whakaaro ki te ārai, i te reira e kore e tata te tīariari. Noatia, he reira e minaminatia ki te karo i aua āhuatanga e taea arahi ki "i matao" ira. E noho hauora!