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Syndrome o Gilbert. Tona tātaritanga, hopearaa

syndrome o Gilbert, ko reira hoki te mate? syndrome o Gilbert - te kē haumanu hyperbilirubinemia mahi tino ngawari. E whakaatu ana te mate UGT1A1 ira irakētanga. No te o ia, whakawaeheretia te whākōkī e te UDP. āhuatanga syndrome o Gilbert e te whai ake:

  1. taumata teitei o te bilurbina toto
  2. glyukuroniltransferazy kore Motunga
  3. Ngaro o huringa ate
  4. Tuhinga o bilirubin teitei e tika ana ki te mahi o te phenobarbital

Hoki te wā tuatahi syndrome o Gilbert kitea i roto i 1901, tākuta French Gilbert Nicolas Augustin me Lereboullet P. tāutuhia ratou te syndrome rite "he cholehemia whānau". I muri i taua, i te whakaaro reira he torutoru ingoa, engari mutu i runga i syndrome o Gilbert. maha puta tenei syndrome i roto i nga tangata 25-30 tau te pakeke.

Tohu angamaheni mō mate

I roto i te tangata, i reira he rohirohi, puta tika colic hautahi o runga. Ko te faaiteraa matua o te syndrome ko te manukanuka, me te tae peita. I te tahi taime tupu te reira e kore te mea kite te yellowness, a ka ako te tangata e pā ana ki te mate i muri anake puritia reira he rauropi matüora. E rua ngā momo o te mate: wā, me te mau tonu. Ki te te ngāwari tinana he tangata koutou tinana, kia puta te jaundice. I tua atu, te tūkino waipiro, kia hemokai he "tīmata" mo te whanaketanga o te mate.

tātaritanga syndrome o Gilbert.

bilubirin tairanga i roto i te mate, kia kia i te taumata o te 21-51 mmol / l, ai ko reira taea ki te whakapiki ake i te taumata o te 85-130 micromoles / rita. Ki te tautuhi i tenei mate, e hiahia ana koe ki te haere i te tātaritanga motuhake. E nehenehe te reira o te maha momo.

  1. Test ki te hemokai. whakamahia te nuinga kai ngako-iti, i te iti rawa - te nohopuku mo 48 haora. Ko te kupu te kukū o bilirubin i roto i nga piki toto.
  2. Test ki pentobarbital. Ko te whakamahi o tenei rongoā arata'i ki whakaongaonga o te glyukuroniltrasferazu mahi paru, reira whakaiti i te taumata o te bilirubin.

maimoatanga o te mate

Tetahi maimoatanga motuhake, i roto i te whānui, kahore, no te mea te mea he āhuatanga o te rauropi, e kore te mate. Just mate kawenga contraindicated anō, me whai i te reira i te kai motuhake. kia rāhuitia inu waipiro mo te tangata penei no te mea e taea e ratou te whakamahi arahi ki te whanaketanga o te mate. Ko te mea utu te haamana'oraa e i roto i nga take o te syndrome o Gilbert e kore te mea e tika ana ki te paopao ki kano. I roto i whakahau amplification tākuta jaundice he tetahi kai, whakaritea huaora therapy te.

pānga syndrome o Gilbert

Ko te hunga e kitea syndrome o Gilbert, te pānga o te moni, me te pehea e pā te mate te ate. e kore e taea e ētahi pānga e i te katoa, engari te mea pai ki te mahi i ultrasound o te ate, me te he whakamātautau toto mo bilirubin. Ki noho tonu ki runga ki te rapunga o syndrome a Gilbert te ate, e hiahia ana koe ki te piri ki te kai, ka whakawhāiti koe ki faaohipa. I te tahi taime e taea te pānga o te mate faaite mai rite steatosis ngarahu molengofuá. Fele, kua rite enei pānga i roto i nga tangata. Na reira, nga tangata e mate ana i te syndrome Me ki te aroturuki ratou hauora.

He aha e nga matapae hoatu te mate?

Ka taea te whakaaro i tēnei mate he kē o te täkupu. E whakaaro ēnei iwi ki te kia āhua hauora, te atu pera i roto i te maimoatanga motuhake e kore e ratou hiahia. Ahakoa te meka e taea te tonu hyperbilirubinemia mo te ora, e kore e syndrome o Gilbert arahi ki te mate. He he he pea o disorders psychosomatic, me cholelithiasis. E kore e puta i te mau hopearaa o tenei mate noa 20 tau, engari haere tahi tonu i te tangata, te atu e taea te mahi tauwehe whakapapa. Ko te mea tino nui, ko te e kore te tino pānga tenei mate i runga i mahi a te tangata.

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