A Felty Syndrome: tohu, Diagnosis

I raro i syndrome o Felty e pā ana ki te pōauautanga o kaikōiwi, e puta i roto i te% 1 anake o tūroro katoa ki te mate. Fever, uaua atrophy, ähua me te susceptibility ki mate hopuhopu āhua - katoa o enei āhuatanga te tikanga haere tahi syndrome o Felty. hāngai Pathology tātaritanga te i runga i te hītori o te kaikōiwi, te mahu'inga no tawhā taiwhanga. Treatment Ko tā te horomanga o corticosteroids, splenectomy. Hoki te wa roa i te māuiuitanga āhuatanga e natula pahuhu me te pikitia haumanu. I roto i te 1929, whakaahuatia AP Felty te raruraru. Ake mai i rerekëtanga te mate hei nosology motuhake.

Felty syndrome: he aha te mea te reira?

tautuhi ana te mate e te aroaro o toru pathologies tukutahi: te kaikōiwi, kōateate rahi me te leucopenia (iti ma pūtau toto). Kei te nuinga o pāngia tenei syndrome i roto i te iwi pakeke atu i te 40 tau, te tikanga i roto i te takoto ataahua.

Tohunga whakaaro e te pūtake o te mate, ko te tukanga autoimmune. puta te reira ki te whai wāhi tika o te kopa lymphoid me te hanganga muri o complexes ārai me te paturopi motuhake. whakakitea māuiuitanga rite neutropenia ki te whakaiti whakahauanga i roto i ātete ki te nuinga o mate, a ka puta ratou - ki nui. Na tenei ra ko te splenectomy (tango o te kōateate) Kei te mohio anake tikanga whai hua o te maimoatanga.

āhuatanga syndrome o Felty e nui kanorau, maha mohiotia. kia mua raruraru e rave rahi tau (5 ki pā ana ki 10) mate pera-ka karanga polyarthritis rheumatoid ki te whai wāhi tukutahi i roto i pathological hononga tukanga interphalangeal, ki rerekē nekehanga o te pakeke.

I te tahi atu te ringa, kua oti te whakarite te nuinga o tūroro ki tenei tātaritanga e faaiteraa angamaheni o kiko tūhonohono. kia he kirika, te hanganga o nodules subcutaneous, myocarditis, mate o taimaha, poliserozita tenei.

Ko te take matua

He unknown te etiology o te mate. Ehara i tūroro katoa ki te tātaritanga o "kaikōiwi" Kei te whakawhanake i tēnei māuiuitanga. I roto i te hinu wheua wheua o te tangata hauora e tonu whakaputaina e ngā pūtau ma toto. Tūroro ki tenei syndrome, ahakoa te tohanga āhua iti, kua hanga e hoki leukocytes. ai ratou whakaemi i roto i rahi i roto i te kōateate.

He aha nga tohu haere tahi syndrome o Felty i roto i ngā pakeke?

• syndrome Articular (kaiponapona o te hononga iti).
• Te whakanui ake i te rahi o te ate.
• lymphadenopathy whānui (pāngia i roto i te 50% o te wā).
• Ko te hua whakamua i roto i te rahi kōateate (rite whakaritea e te palpation).
• Polyneuropathy.
• Ähua i runga i te kiri, mariao i te shins.
• Haaparare i kakakīrehe pūkahukahu.
• nodules Rheumatoid.

te āhuatanga i runga katoa hanga reira taea ki te tātari syndrome o Felty. E whakaaturia ana te tohu o te tūroro katoa rerekē. Hei tauira, kitea ētahi wā whakarahi o te kōateate e anake i roto i te wāhanga i muri mai o te whanaketanga mate.

tātaritanga

Ko te pūtake mo te haamauraa whakamutunga o te tātaritanga haumanu o te huinga tukutahi o splenomegaly me kaikōiwi. āhuatanga whakamātautau toto e anemia, leukopenia, neutropenia. te nuinga te immunoassay RF kitea titers tiketike, te CEC, te aroaro o paturopi antinuclear. E ai ki nga hua myelogram pāngia hyperplasia wheua myeloid te ki te neke ki ngā āhuatanga pūtau teeki. He tino pea ki te whakarato iti mōhiohio tikanga Instrumental o tūhuratanga (MRI, CT, ultrasound o te hononga iho). He tino nui syndrome o Felty ki te rerekëtanga ki cirrhosis me sarcoidosis.

te mau parau tumu Basic o te maimoatanga

Therapy, i roto i tenei take tā te huarahi whānui. tukinotia kaikōiwi te rite paerewa. Therapy auau mate, me te rumati tae atu taero e te tauturu i te rūmātiki ( "Azathioprine", "MTX").

Tūroro ki mate nui e tūtohu ana ki te hanga werohanga ia wiki o te take, e whakaihiihi ana granulocyte koroni. faarahi te reira i te maha o ngā pūtau ma toto.

kia whakaiti taero Basic te tohutanga i haere tahi tika rumati, Felty syndrome. Ko ētahi o ētahi o ēnei: "Methotrexate", "Penicillamine".

He whai hua Glucocorticoids anake i roto i toketaá tiketike. Te kore, kei te piki haere te reira i te tūponotanga o te matahoki. I te tahi atu te ringa, te whakamahi roa o glucocorticoids taea arahi ki te whanaketanga o mate intercurrent.

Ko te paearu mo te whai huatanga o te therapy:

• Te whakanui ake i te maha o granulocytes ki te 2000 / mm.
• Whakaitinga i roto i te pā o pōauautanga hopuhopu o te natura.
• Tuhinga o whakaeke kirika.
• Tuhinga o keha i runga i nga faaiteraa kiri.

A, no te tūtohutia pokanga te?

Pehea atu koe e taea e hinga syndrome o Felty? Treatment i pokanga tūtohu te ki te i whai hua therapy tarukino no o tetahi take, kua contraindicated reira ranei. I roto i tenei take, ko reira te tikanga he pātai o splenectomy. He mea nui ki te mahara e roto i te 25% o ngā take o te neutropenia mai anō ko muri i tenei tukanga.

I raro i splenectomy tikanga pokanga, i roto i te mea tino te tākuta ranei wāhanga tango te kōateate. I teie mahana, i reira e rua e taea o te tukanga taua: splenectomy laparoscopic me tuwhera.

whakamana Laparoscopy Kei te whakamahi i rehunga whānui. I roto i tenei take, Ko tā te mahi tono o te mea angiangi ki te kāmera i runga i te mutunga, i huaina nei ko te laparoscope. hanga te taote e rave rahi vahi iti i roto i te puku i roto i nei whakamōhio taputapu mō whawhe muri. Te wā whakaora, rite ki te tikanga, e kore e rapua e nui te wā.

Open splenectomy tā te kokoti nui i raro i te rara, i roto i nei tango te tākuta te kōateate. I muri i tango o te tinana kaha o te tinana ki te tātari i roto i te huakita me huaketo i te toto te mārika i iti.

pōauautanga taea

Pōauautanga he mate tino onge, me te kia whakaatu ano i roto i te puka o te kōateate whaturama, te whanaketanga o pera-ka karanga takawhita tomokanga, gastrointestinal toto puhoi puta mate tuarua.

mutunga

syndrome o Felty - he mate ngā onge, engari he pōauautanga o te rōpū katoa o pathologies i tenei ra e pāngia uaua. E kore tenei tikanga e taea tatou tau'a ore tona maimoatanga, me te kore ki te rapu i te tauturu tohu ki te tākuta e tika ana. kia mōhio tohu Paraimere katoa, me te riro i te take mō te rapu tohutohu i te mātanga. Te kore, kei te piki haere te reira i te tūponotanga o ino o te kāwanatanga whānui, me te whanaketanga o feunga mōrearea ki fifi hauora, e ngā whaturama o te kōateate iho. Kei te mohio te kōwhiringa maimoatanga whai hua anake i teie nei rite te splenectomy.

Te ti'aturi nei tatou e, e kia tino whai hua ki a koutou i te mōhiohio e whakaratohia ana katoa i roto i tenei tuhinga i runga i te kaupapa. E noho hauora!