He aha te mea te reira - he syndrome Rokitansky-Otto Küstner? Syndrome Rokitansky-Otto Küstner: take, tohu, maimoatanga

Surrogacy taea tamariki ki nga wahine nei hoki take hauora e kore e taea e hapu i te tamaiti i runga i to ratou ake. Ratou maha, kia rite ki nga tatauranga, nui haere i tau ki te tau. Ko tētahi o nga take mo te pīra ki te ratonga o te whaea a Maata ko Rokitansky-Otto Küstner syndrome. Ka nga take o te mate, te tohu me te tikanga taketake o te maimoatanga e lāulea ki roto i tenei tuhinga. Ka ako ano hoki koe ranei te wahine ki tenei syndrome whai tamariki.

āhuatanga māuiuitanga

Syndrome Rokitansky-Otto Küstner-Meyer-Hauser - he mate gynecological onge. Kei nga ingoa o pūtaiao nei aroaro te whakamārama taipitopito o te māuiuitanga i tona ingoa. Ano i roto i te tuhinga hauora i reira he taurite o te mate: atresia tara, aplasia o te kōpū. Heoi, e kore ratou e whakaata maumaui katoa i roto i te tinana, angamaheni o te syndrome. I tua atu, kia puta atresia tara tika ki mumura tafa ranei. E mea pinepine, ki te ingoa tonu o te mate whakaiti i te ingoa tuatahi e rua o nga kaiputaiao te wā "syndrome MRKH" ranei.

huru no te māuiuitanga e ngaro oti te kanohi ranei o te kōpū, me te 2/3 o te tenetene. I roto i tenei take, i reira ko te whanaketanga tonu o te ovaries me kikokiko. rongoa hoki ngā āhuatanga fakasekisualé Tuarua (huruhuru tinana i runga i te momo wahine, uma). pāngia Rokitansky-Otto Küstner syndrome te uaua (kotahi take ia mano 5. Girls whanau hou).

mōhiohio hītori

Ko te whakaahuatanga tuatahi o te rā mate hoki ki 1829 tau. tuhia rata German Carl Mayer e te maha haere tahi aplasia tara i te momo o abnormalities whanaketanga. A iti i muri mai, i roto i te tau 1838, i te kairangahau mate i Austria Karl von Rokitansky whakaahuatanga syndrome tāpiri. takoto ia e ki ko ano hoki tenei mate kōpū ngaro, ovaries engari te pupuri i te kaha ki te mahi tino. I roto i 1910, te rata German German Kyustner haapoto te mōhiohio e wātea ana i runga i te mate, tāpiri ia ake kitenga. Te rata mātai whakaahuatia tauira ngā auau ki aplasia uterine malformations whanaketanga tākihi. I roto i te 1961, Professor Zhorzh Hauzer i Switzerland te whakaaro e te wā "Otto Küstner Rokitansky-Mayer-syndrome". whakaputaina Scientist ana kitenga maha o tūroro ki tenei tātaritanga, i kumea ana whakarongo ki te oreraa ki hormones tane i roto i tūroro. I roto i te 1977, Houser tuatahi aroaro he whakaahuatanga o te kē mohiotia o māuiuitanga. Homai te takoha nui o pūtaiao, i te ingoa te syndrome mō discoverers o wha ingoa.

Take o te mate

Ahakoa i roto i te wā embryonic fetal hē kikokiko takoto e tohu Otto Küstner-Rokitansky syndrome. Photos o ngā tamariki ki tenei tātaritanga i muri i whanau e kore e rerekē i te hunga o ratou hoa hauora. E ai ki te ariā o Muller, whakawhanake nga whekau sex kukune i roto i te rua o nga marama, i muri i haputanga. Ko te pānga o te āhuatanga kino i runga i te tinana o te hapu i tenei wa e taea meinga tini o nga mate i roto i ngā tamariki. I runga i te takanga o te syndrome pānga hoki tūhonohono kiko dysplasia kukune i roto i nei te ngangau o tona hanganga puta. huringa pathological arahi ki te whanaketanga o whekau hapa, kotahi faaiteraa o e ko te syndrome Otto Küstner-Rokitansky.

He aha ngā āhuatanga whakaawe i te takanga o te mate i roto i te tamaiti i roto i te hapū?

1. toxicosis kaha.
2. HIV i roto i te whaea.
3. Ko te ati o te materoto.
4. Tango etahi rongoā (pērā i corticosteroids).
5. tūkino waipiro.

E kore te te syndrome whakarōpūtia rite mate tuku. Heoi, i roto i te mahi haumanu i reira he take te wahi pāngia te māuiuitanga e rave rahi wahine o te whānau kotahi.

faaiteraa haumanu o te mate

Kei te tīmata Otto Küstner-Rokitansky syndrome ki faaite mai i roto i te pūhuruhurutanga, ka reira pūhuruhurutanga o rauropi. Ko te kōtiro āta häunga u, te huri i te ahua, i reira he huruhuru te tinana i roto i ngā wāhi tupu. Korerotia āhuatanga fakasekisualé tuarua e kore e faati'a ai whakapae raruraru hauora. He maha ngā kōtiro ite mamae wā i roto i te rohe puku o raro, pouri i roto i te hoki o raro. Heoi, ko te ngaro o te paheke arata'i ki te rapu i te tauturu i te rata mātai. Ko tētahi atu take mo te haerenga ki te mātanga kia he raruraru o te āhua tupu. maha hua ngana tutuki o takoto i roto i te whētuki ki te perineum whaturama ranei o te tōngāmimi. Faaiteraa o tinana underdevelopment taea te mahi rite te kōpū fare ki korere kākano rerekē. Tata 40% o te syndrome sex MRKH ataahua ngā ki malformations o te pūnaha mimi.

whakarōpū o mate

Ka rite ki te maha atu kōhikohiko o te whanaketanga embryonic, he nekehanga rerekē o te pakeke Rokitansky-Otto Küstner syndrome. whakaritea te kaha o ia o ratou e te pakeke o abnormalities fetal. E toru ngā āhua o te mate:

1. syndrome MRKH Angamaheni (64% o te wā katoa). Kei te āhuatanga i te reira na roto i te aplasia o te kōpū, me te tenetene.
2. syndrome MRKH mohiotia (24% o te wā katoa). I roto i tenei mate, nga kotiro ngaro kōpū me tara, i reira te mea he pōrearea o te ovaries.
3. MURCS-rōpū (12% o te wā katoa). Ko te puka tino nui o te syndrome, āhuatanga nei i te disorders whakarārangitia i runga ake me te kīnaki e te whanaketanga rerekē o te tuahiwi tenei.

Puka o te mate whakatau te rautaki haumanu, me te āwhina tākuta hanga he matapae o te ora.

tikanga o te tātaritanga

He aha te tirohanga he tika ki te whakaū i te syndrome Rokitansky-Otto Küstner? e kore e anake te paearu mō te tātaritanga Tohu o mate. haamata whakamātautau manawanui ki te tirohanga ataata. I roto i te 75% o te wā, e kore te reira e whakakitea tetahi maumaui, no te mea hāngai te āhuatanga tuarua ki ngā tikanga. Na, he haki i runga i te parahiraa gynecological. kawea te kotiro ki te tātaritanga werewere e i roto i te tikanga o Tārewa. Hoki angamaheni syndrome poto tara (ki runga, ki te 2 cm), e kore te mea nei i te mutunga o te awa cervix. Ko tētahi atu kōwhiringa tātaritanga ko te whakamātautau rectal, i roto i nei nga whatumanawa te tākuta pūkano, me te uterine kōhao. hanga i tēnei tikanga e taea ki te aromātai i te tohu o te hanganga o whēkau.

inenga auau o basal pāmahana tauturu whakatau i te wāhanga o te huringa te paheketanga ki te whakaū i te mahi tonu o te ovaries. I tua atu, whakatakoto te tākuta whakamātautau toto mo hormones, MRI me ultrasound papatoiake. I roto i te wā tino nui kia rapua e tātaritanga laparoscopic.

Methods o te maimoatanga

He he kotahi anake te ara ki te whakaora Rokitansky-Otto Küstner syndrome - kirihou tupu. Mahi i runga i te hanganga o te tenetene ka karanga colpopoiesis ki ona rata tiaki i haere ki te rau tau XIX. I te tīmatanga, whakamahia te mahi ki te hamani wahine ki mahi kōpū ka ora taua. I roto i enei tūroro kihai i haere mai i te toto i te tinana, a āta whiwhi i roto i te kōhao puku. Ka rite ki te hua, kua pāngia e ratou ki tukanga neoplastic, i haere tahi nei i te mamae kino, me te ngā pōauautanga.

I tēnei wā e pupuri ana colpopoiesis ara e rua:

1. Roha o te tara ki te awhina o te poihau te hangatanga. e te mahi i te wa roa. Ko taea Ko tōna whakatinanatanga anake, ki te te roa tara kore te mea iti iho i te 4 cm.
2. Hanganga wahi neovaginy o te kopirua sigmoid kiri ranei o te puku. hangarau Modern tukua ki te whakatika i nga mea kohakore, kahore vahi puku - laparoscopically. maha hiahia Doctors tenei tikanga, te hanganga o te tara tāwhaiwhai.

Ko te tau pai mō te colpopoiesis ko te wā i 16 ki te 21 tau. Tenei wa, te koinei te whakamutunga o te rauropi. Ko te whakaaro kapu o te kirihou tara - taea wahine ki te oaoa i te ora sex tonu. Kia kore ai tona imperforate kore e whakarerea sex auau, ia wā haere bougienage tukanga.

Pōauautanga i muri i te pokanga

He aha e nga pōauautanga i muri i te pokanga kia tūtaki tūroro ki te tātaritanga o "syndrome Rokitansky-Otto Küstner"? Treatment o te mate e ētahi wā haere tahi e tetahi hopearaa kino. Colpopoiesis - Ko te mahi nui tenei. Ka rite ki ki tetahi atu ahua o te pokanga, ko reira taea te whanaketanga o pōauautanga. I roto ia ratou, he sepsis me peritonitis te noa tino. Ano, he maha tūroro i muri i te akoranga o te maimoatanga, pāngia taiepa neovagina hononga te taote. whakawhanake ana tēnei māuiuitanga e tika ana ki te kore o te ora sex auau. Na reira, kaha tūtohu tākuta e kore wahine ki te paopao sex.

Matapae i muri i whakaora

Huringa i roto i te tinana e puta i roto i nga wahine ki te tātaritanga o "Rokitansky-Otto Küstner syndrome" e kore e tukua ki te kawe i roto i mahi uri i roto i te ara tūturu. Heoi, tikanga hou o IVF me tokoni surrogacy taua tūroro whai tamariki koiora. tata kua kauwhautia Scientists hua pai o te whakahaeretanga o transplant kaituku kōpū. I muri i te ia, pea, transplantation o te tinana e āwhina i te wahine ki tenei mate haavare i runga i to ratou ake ki te mau tamariki.

Pākoko me syndrome Rokitansky-Mayer-Otto Küstner

Ka taea e ahau tamariki ki tenei mate? whakatika ana tēnei pātai i te wahine tokomaha te hunga e fehangahangai ki te māuiuitanga. Maoro ranei i muri mai, e hiahia ana ia o ratou ki te tamata i runga i te tūranga o te whaea. Te nuinga o nga wahine ki tenei syndrome kore e taea e te tamaiti. Ki te kei te mahi i te ovaries tikanga, na tohunga whakaaro tūroro i puritia ana ki nga ratonga o te whaea a Maata. I roto i tenei take ka hapu te pēpi te?

I roto i te wāhanga tuatahi o te hōtaka whaea a Maata, me te wahine kino whakaritea te raau taero hormonal. Ko te whakamahi o te raau taero i roto i te tetahi wā taea ki a koe te tukutahi ratou huringa paheketanga. Na āwenewene inseminated te wahine o te syndrome hua MRKH ki parāoa o tana tane. I roto i te torutoru ra o ratou "tupu" i roto i te reo e ka tāwhai i te āhuatanga o te korere kākano. I muri i nga ra e toru, kei te tīmata tohunga teuteu ki mua-implantation: whakatau te sex o te ira, te aroaro o hē pūira me mate tuku. I te rima o nga ra e whakawhitia ahu kukune ki te kōpū o te whaea a Maata. I roto i ētahi wā, he podsazhivanie rua, hei tauira, i runga i te toru me te rima o nga ra.

Ko te maha o embryos kia rerekē i runga i te kounga o te rauemi ira, tau o te manawanui rānei whakawhitia. I te tono o te wahine, te hua manu kāore amohia e cryopreservation tukanga. Ka rite ki te hua o tenei haputanga ki te ao i roto i te 9 marama i reira ko te pēpē hauora. Heoi, kua rua kaitautoko me hoariri tenei tukanga.

Me whai whakaaro Motuhaketia surrogacy. I roto i te maha haumanu motuhake reira he turanga o nga wahine pera-ka karanga, nei e pai ki te whakarato i te ratonga rite. Ko te tikanga ko reira taitamariki, kotiro hauora. Ko tētahi o nga take mo te paitanga ki te whare hauora taua ko te syndrome Rokitansky-Otto Küstner-Meyer-Hauser. metua vahine a Maata Photos heke mai ano e taea te kitea i roto i tenei pātengi raraunga. Te tukanga katoa, i te kōwhiringa o te biomamy pea, me te whakamutu hapūtanga, ngā kaiwhakahaere mana pokapū. Na ko reira pai ki te whakapā atu i te tohunga, kaua ki te whai wāhi i roto i te rapu mo te whaiaro. Anake i roto i tenei ara e taea noho māia i roto i te hauora o tō pēpi i mua nei.

Hei whakarāpopoto

Syndrome Rokitansky-Mayer-Otto Küstner - ko te mate iranga āhuatanga e ngaro hypoplasia ranei o te kōpū, me te tenetene. e kore e maha ngā kōtiro i mua i pūhuruhurutanga noa mohio e pā ana ki ngā raruraru hauora. ai Amenorrhea ratou kia kite i te rata mātai. Ko reira i te fariiraa i te tohunga ratou tuatahi riro mōhio o te oraraa o te syndrome taua. I runga i te ringa kotahi, he mea angamaheni ki maldevelopment o te kōpū, me te puta tenetene, me i te tahi atu - te aroaro o āhuatanga sex tuarua. I teie mahana, i reira e rave rahi kōwhiringa maimoatanga mō mate. Kei te pai ake tonu katoa o ratou, ka kō. Ko te therapy o te mate, ko te ki te tango i te koha e kirihou tupu. Ka rite ki te hua, e taea te tiki i te manawanui whakakahoretia o nga raruraru hinengaro, me te whaiaroaro, te oaoa i te ora, me te ara i ngā tamariki. Ki te whakaaro ki te wāhi muri, e titau te reira i āwhina o te whaea a Maata.