Malformation iaia: take, tohu, tātaritanga, me maimoatanga

Ki te raru i roto i te tukanga o te whanaketanga embryonic ko te hanganga o te pūnaha circulatory, i hanga te malformation iaia te. Ko te hononga hē o nga uaua me pera, e faaite ake i roto i te taiohi tenei. Te reira i katoa tīmata ki pāhoahoa, migraines me haurangi. I roto i ngā take kino, whai haurangi tamariki.

whakamāramatanga

rerekē hanganga iaia puta noa i te pūnaha circulatory. Ko ētahi nui, ko etahi taiepa uaua, kua vaolo etahi, engari kua hono katoa ratou ki tetahi ki tetahi i roto i te raupapa ngā. Ki te hoki etahi take i pakaru te natura whakapumautia o te raupapa e, te conglomerates e hanga e oko ore, ka karanga malformations.

Tikanga, tenei mate congenital o take unknown. puta te reira i roto i iwa i roto i o te rau mano hou i ia tau. Ka taea e meinga malformation tahae syndrome, kōpeke te ua, me te kiko roro, ki te hanga i te aneurysm me meinga he patunga me te pakaruhanga toto meninges. Nuinga o ngā wā pōauautanga tupu i te tau pakeke, i muri i wha tekau nga tau.

whakarōpū

He maha ngā puka e taea te tango i te malformation iaia. Hoki ratou whakamahi systematization whāngai i roto i 1996 te ISSVA whakarōpūtanga American. Ko tōna rerekētanga taketake i te tahi atu whakarōpūtanga - te wehenga o nga kōhikohiko katoa i roto i te pukupuku, me te malformations.

1. pukupuku iaia:
   - hemangioma aruaru (puta i roto i te kōhungahunga);
   - hemangioma congenital;
   - bunchy hemangioma;
   - veretenopodobnaya hemangioendothelioma;
   - kaposhiformnaya hemangioendothelioma;
   - riro e te puku.
2. malformations:
   - capillary (telangiectasias, angoikeratomy);
   - venous (tāmutumutu, glomangioma, Mafuchchi syndrome);
   - waitinana;
   - matua;
   - arteriovenous;
   - ngā.

Malformation o uaua

Venous malformation he whanaketanga rerekē o rua, aru e ratou toronga pathological. Ko te reira i te noa tino i roto i ngā momo katoa o malformations. Ko te congenital tenei mate, engari kia whakaatu ano i roto i te tamarikitanga, me te i roto i te pakeke. Hurihia te wāhi o te oko e taea e tetahi: he io nahanaha, whekau, kiri, wheua uaua ranei.

pea malformations venous i runga i te mata ranei i roto i te teka tinana kia taratahi nui ranei totoro i roto i te maha o ngā wāhanga tinana. I tua atu, i te ofi ange e takoto ratou ki te mata kiri, te atu kukū te tae taonga.

Nā ki te āhua rerekē me te tae e taea e raruraru ki hemangiomas. Hoki tātaritanga pārōnaki pēhanga rawa iti ki te wahi whakarerekētia. He ngohengohe, me te ngāwari ki te huri i te tae malformations. I roto i te take o te takanga o oko toto rerekē hohonu i roto i te tinana tangata waho māuiuitanga kore e taea te whakaaturia.

Fakataha ki te tipu o te tamaiti, me te nui haere malformation, engari i raro i te mana o ngā āhuatanga keu, pērā i te pokanga, whētuki, mate, taero hormonal, tou haputanga ranei menopause, ite tipu whwhi tere o oko toto.

Chiari malformation

Tenei malformation iaia, āhuatanga nei i te tonsils cerebellar iti-e takoto ana. whakaahuatia te mate i roto i te mutunga o te rau tau rata iwa Austria Hans Chiari, i roto i tona honore, a ka huaina te āhuatanga. tāutuhia e ia etahi o nga momo tino noa o tenei Pākatokato. Nā ki te puku wāhi iti haukoti i matamua inu i te roro ki te ua, hanga reira pēhanga intracranial ake te, me te whakaoho i te whanaketanga o te wairoro.

Chiari momo malformation whakaahua ana te displacement tonsils cerebellar iho a aki ratou i roto i te Magnum puta iti. Tenei whakaritenga ai te roha o te awa filosilivá, e hauora faaite ake i roto i te tino. Ko te tohu tino noa he ānini, tinnitus, tere tere ka haere ana, diplopia, wahapū waimaero, horomia raruraru, a ētahi wā ruaki. Hoki taiohi āhuatanga e mamae heke me te pāmahana tūtohutanga i roto i te hawhe o runga o te tinana, me te wahi.

whakawhanake Chiari malformation momo tuarua ki te nui haere puta iti rahi. I roto i tenei take, e kore e nga tonsils cerebellar taka, a taka ana ki reira. arata'i tenei ki kōpeketanga o te ua, me te roro tuarongo te whakaatu i. I te wa ano he tohu taea o te pupuri inu i roto i te roro, melé ngakau, pakaru o embryonic wahi kūnatu me te pūnaha urogenital.

ua

Malformation o te ua - ko te mate onge e tika ana ki te myelopathy whakamua. malformations Arteriovenous hiahia tūnga i waenganui i nga rau ranei takoto anga pakeke i runga i te mata hikumārō o te roro i roto i te tuaiwi rei lumbar ranei. he noa i roto i nga tangata pakeke te māuiuitanga tino noa.

Ko te mate rite nga tohu o te sclerosis maha, me te taea te tomo i te toketā neave haavare. puta te ino koi i muri whaturama o oko toto, me te toto ki te wāhi subarachnoid. E kitea tūroro disorders tairongo, me te nekeneke wāhanga, taupatupatu o nga whekau papatoiake. Ki te hono tohu cortical, te atu rite ALS (Amyotrophic sclerosis lateral) hoko i te mate.

Ki te amuamu āhuatanga o rerekē disorders neurological rua te manawanui, me te whakapae i te tākuta malformation iaia, me te whakahaere i te tirohanga ataata o te tuaiwi. ka puta nga tohu o te iaia lipoma me he wāhi o nui haere ähua. kia tonoa he tangata pērā ki te atahanga te kōwarotanga autō myelography rorohiko ranei. Tenei ka tukua ki te manatoko i te tātaritanga.

tohu

titiro malformation iaia rite te poma wā he pītara ki te hama ranei ēngari i roto i te ringa o te tamaiti - e kore tetahi tangata e mohio ka e timata kino. Ahakoa te meka i te mate ko te Pākatokato congenital, haamata te reira ki te whakaatu iho nui i muri. E rua ngā momo o malformations iaia rere:

- toto (70% o ngā take);
- torpid (i roto i te toe 30%).

Tetahi o nga kōwhiringa kore e taea te whakaaro ātaahua hoki te tangata ki tenei tātaritanga. I roto i te take o te rere hemorrhagic te manawanui he pēhanga toto tiketike, a ka he iti te wae iaia me te kei i roto i te kaki. tupu tetahi hawhe o te iwi ki te hemorrhagic patunga momo o te malformation e tika ana ki te hauātanga ranei te mate. faarahi te mōrea o te toto ki te tau, me nga wahine he take atu he hapū me te whanau.

Ki te oho pai te tangata te patunga tuatahi, ka ki tūponotanga 1: 3 i roto i te tau ka anō-toto. Na ka te tuatoru. Kia aroha mai, i muri i toru wāhanga, torutoru ora. Tata hawhe o tūroro i faingataa āhua ki te hanga i te pakaruhanga toto intracranial, hematomas ranei whakauru podobolochechnyh tamponade me roro ventricles.

Ko te kōwhiringa tuarua ko te rere nui, e takoto hohonu i roto i te uho kaka malformation iaia. He tino angamaheni ona tohu:

- hihiko takiri te aroaro o te whakaeke epileptiform ranei;
- pāhoahoa nui;
- te aroaro o tohu rite ki te puku roro takarepa.

syncope

Tata iwi katoa ki malformations iaia kei roto i te roro, e maoro, i muri puta syncope (arā, syncope). Ko te tika ki te heke rangitahi i roto i te tohanga kaka tenei. I roto i te mea ha ma syncope manawanui, hipoki ki te werawera makariri, ona ringa me waewae i matao, pini ngoikore, me te manawa pāpaku. roa te whakaeke e pā ana ki e rua tekau hēkona, me i tona mutunga e kore e te manawanui mahara tetahi mea.

Katoa tau i reira e neke atu i te hawhe i te miriona take hou o syncope, me te wahi iti o ratou anake kua mārama te hononga take-a-pānga. Ka taea te meinga Syncope i whakaongaonga nui o te pakohu kakī, roro trigeminal ranei karere glossopharyngeal, ture o te pūnaha io iti hoki autonomic, raruraru manawataki ngakau me, o te akoranga, malformations iaia. pera rerekē me uaua whakarato whakanuku o toto, me te whakatere i tona rere. Ka rite ki te hua, e kore e whiwhi i te roro nui kai tōtika, whakakitea nei disorders o te mahara.

pōauautanga

i mua i Ahakoa te malformation faaite mai ake hauora i roto i te tangata e huna e whakawhanake ari pathological tina heke. Ko tenei e tika ana ki hypoxic wahi kiko roro, te reira te ma'ii'o me te mate. Tei runga i te wāhi o te wāhi kua pā kitea te he tohu āhuatanga rahi (abnormalities kupu, kiwi e, nekehanga tūao, maramarama me te t. N.) taea e haurangi haurangi.

timata kē pōauautanga kino i roto i te pakeke. oko toto rerekē i taiepa kikokore me e atu e pängia ana ki piere, na tūroro ki malformations atu noa whiu rere pūroto. conglomerates nui pera me uaua kōpeke te kikokiko a tawhio noa ratou, meinga wairoro. Ko te tino mōrearea he toto e tika ana ki te whaturama o te maha oko. kia kia whai te reira ranei nunu'a whakamate, ka mutu ki iti ranei kahore nunu'a. Te reira i katoa tei runga i te maha o te toto rere. Hemorrhagic patunga Ko nui iti whaihua outlook me kia auau ai i runga i te wā.

tātaringa

e kore e whakamātautau neurological tuatahi whakakitea tetahi abnormalities i roto i te iwi ki te malformations iaia. Ko te tikanga ko tā te reira whai me te whakamātautau rawa tino ki te tāutu i maumaui. Ki te amuamu te manawanui o pāhoahoa nui auau, tremors, raruraru wā o te mahara, me te kite waimaero haere ranei, ko reira he wāhi ki te tonoa a ia ki te whakahaere i neuroimaging. Mämä noa iho, he rorohiko te kōwarotanga autō ranei atahanga o te roro.

E whakaatu ana te hanganga iaia tino kiko, me te tika i te rerekē angiography. Hoki tenei manawanui i roto i te iatuku kakī noa i patia radiopaque wai, me te hanga i te raupapa o ngā matā. he maha o pōauautanga me ngā pānga taha tenei tikanga kua, reira, he hāngai anake i roto i te take o te fifi i roto i te hanga i te tātaritanga.

Hei tiro i te tere, te ahunga me te auau o te rere toto ki te huringa wā, te whakamahi i Doppler ultrasound. taea tatou tenei tikanga kia kite i te rere toto i waenganui i pera me uaua, ki te whakatau i te momo o oko, ki te whakatū i te aroaro o aneurysms me ētahi atu pōauautanga.

maimoatanga

Ahakoa malformations iaia Nireaha ki te ako? tikanga Treatment whakawhirinaki i runga i te momo o te pīari, tona wāhi, te rahi me te arotahi o te hītori o nga whiu.

E toru tikanga matua o te maimoatanga:

- tuwhera pokanga;
- embolization minimally urutomo;
- kore-urutomo maimoatanga radiosurgical.

Hoki ia o ratou i reira he tohu, contraindications, me te rārangi o pōauautanga taea.

Ko te ngaukino tino he tuwhera pokanga. I roto i te tikanga ki te tiki ki te ahi, kia whakatuwhera i te pakohu roro, klipiruyut oko, me te whiti ratou. He taea te whakatinanatanga pērā i roto i te malformation take kei runga i te mata o te roro, me te he āhuatanga iti. Whakamātau ki te tae te pāpaka hohonu-noho kia hua i roto i te kino ki ngā faufaa me te putanga mate.

Aha e taea te mahi ki te te hohonu malformation te manawanui? Treatment He embolization endovascular. Ko te tukanga tika ngawari, i roto i nei he oko nui e kai te tokamāhurehure rerekē, whakaurua he pū tōngāmimi angiangi i raro i te mana X-ray tenei ka riro te tākuta ki te malformation. Na iaia lumen tarukino hypoallergenic whakahaere e whakakiia ana te wāhi me poraka rere toto e wātea ana i roto i tenei rohe. Kia aroha mai, e kore e tenei tikanga whakarato te haapapûraa tino e te oko ko tino obliterans. Na reira, tino maha te whakamahia te reira rite te maimoatanga tautoko.

Ko te tikanga tino matatau mō te Vascular malformations riro mahi mā te whakamahi i ipurangi maripi (radiosurgery). Ko te ngako o te tikanga, ko te ki te whakawhāiti ki te hapai i hihi iraruke kanga rerekē i koki rerekē. taea tēnei ki te whakangaro hohoro koutou te huringa iaia, kore ai e hāmate kiko hauora. Ko te tukanga o te pakeke o te oko i runga i toharite toto e te marama torutoru. Ko te painga ko te ngaro oti o pōauautanga i roto i te pūnaha io. Ko reira he whāititanga ki te whakamahi o tenei tikanga:

1. E kore e nui ake te diameter whānui o te oko e toru henimita.
2. I roto i te aamu e kore e waiho te patunga atu toto ranei. Mai te taiepa kikokore, me te kore e taea te tu whaturama i roto i te wā i waenganui i te mahi o te tukanga me te pakeke whakamutunga o te malformation.